Gene Gene synonym Ensembl Gene description Chromosome Position Protein class Evidence summary HPA evidence UniProt evidence MS evidence Antibody Reliability (IH) Reliability (Mouse Brain) Reliability (IF) Subcellular location RNA tissue category RNA TS RNA TS FPKM FPKM max in non-specific AADAT KAT2, KATII ENSG00000109576 Aminoadipate aminotransferase 4 170060222-170091699 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA037502 Uncertain Uncertain Plasma membrane, Vesicles Tissue enhanced 0 liver: 21.2 prostate: 11.9 AARS2 AARSL, bA444E17.1, KIAA1270 ENSG00000124608 Alanyl-tRNA synthetase 2, mitochondrial 6 44299654-44313326 Cancer-related genes, Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA035636, HPA061396 Uncertain Supportive Mitochondria Expressed in all fallopian tube: 6.2 AASS LKRSDH, LORSDH ENSG00000008311 Aminoadipate-semialdehyde synthase 7 122075647-122144280 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA020637, HPA020728, HPA020734 Supportive Supportive Mitochondria, Vesicles Expressed in all ovary: 19.4 ABAT GABAT ENSG00000183044 4-aminobutyrate aminotransferase 16 8674565-8784575 Disease related genes, Enzymes, FDA approved drug targets, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041528, HPA041690 Supportive Tissue enhanced 0 kidney: 90.0;liver: 142.4 cerebral cortex: 81.2 ABCB10 EST20237, M-ABC2, MTABC2 ENSG00000135776 ATP-binding cassette, sub-family B (MDR/TAP), member 10 1 229516582-229558695 Mitochondrial proteins, Plasma proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level CAB044063, CAB044065, HPA055175 Uncertain Expressed in all bone marrow: 30.0 ABCB6 EST45597, MTABC3, umat ENSG00000115657 ATP-binding cassette, sub-family B (MDR/TAP), member 6 (Langereis blood group) 2 219209768-219218990 Disease related genes, Mitochondrial proteins, Potential drug targets, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA046723 Uncertain Expressed in all testis: 19.2 ABCB7 ABC7, ASAT, Atm1p, EST140535 ENSG00000131269 ATP-binding cassette, sub-family B (MDR/TAP), member 7 X 75053172-75156732 Disease related genes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA034982 Uncertain Supportive Mitochondria Expressed in all duodenum: 13.7 ABCB8 EST328128, M-ABC1, MABC1 ENSG00000197150 ATP-binding cassette, sub-family B (MDR/TAP), member 8 7 151028422-151047782 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA045187 Uncertain Supportive Mitochondria, Nucleus Expressed in all thyroid gland: 9.6 ABCE1 OABP, RLI, RNASEL1, RNASELI, RNS4I ENSG00000164163 ATP-binding cassette, sub-family E (OABP), member 1 4 145097932-145129179 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB012476, HPA036846 Uncertain Supportive Cytoplasm Expressed in all tonsil: 28.8 ABHD10 FLJ11342 ENSG00000144827 Abhydrolase domain containing 10 3 111979010-111993363 Enzymes, Mitochondrial proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA036991, HPA036992 Supportive Supportive Nucleus, Nucleoli Expressed in all kidney: 31.0 ACAA2 DSAEC ENSG00000167315 Acetyl-CoA acyltransferase 2 18 49782167-49813960 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA042303 Supportive Supportive Mitochondria Expressed in all liver: 254.3 ACAD8 ENSG00000151498 Acyl-CoA dehydrogenase family, member 8 11 134253495-134265855 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA040689, HPA043903 Supportive Expressed in all thyroid gland: 31.1 ACAD9 MGC14452, NPD002 ENSG00000177646 Acyl-CoA dehydrogenase family, member 9 3 128879490-128916067 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA037716, HPA046720 Supportive Supportive Mitochondria Expressed in all skin: 34.1 ACADL ACAD4, LCAD ENSG00000115361 Acyl-CoA dehydrogenase, long chain 2 210187939-210225491 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA010611, HPA011990 Uncertain Mixed thyroid gland: 16.0 ACADM ACAD1, MCAD, MCADH ENSG00000117054 Acyl-CoA dehydrogenase, C-4 to C-12 straight chain 1 75724347-75787575 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA006198, HPA026542 Supportive Supportive Mitochondria Expressed in all kidney: 163.5 ACADS ACAD3, SCAD ENSG00000122971 Acyl-CoA dehydrogenase, C-2 to C-3 short chain 12 120725735-120740008 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA004799, CAB019284, HPA022271 Supportive Supportive Nucleus but not nucleoli, Centrosome Expressed in all duodenum: 56.0 ACADSB ACAD7, SBCAD ENSG00000196177 Acyl-CoA dehydrogenase, short/branched chain 10 123008979-123058311 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041458 Uncertain Supportive Mitochondria Expressed in all liver: 122.6 ACADVL ACAD6, LCACD, VLCAD ENSG00000072778 Acyl-CoA dehydrogenase, very long chain 17 7217125-7225273 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA019006, HPA020595 Supportive Supportive Nucleus, Mitochondria, Nucleoli Expressed in all adrenal gland: 298.3 ACAT1 ACAT, THIL ENSG00000075239 Acetyl-CoA acetyltransferase 1 11 108121516-108147776 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA004428, HPA007569 Supportive Supportive Mitochondria Expressed in all liver: 310.7 ACBD3 GCP60, GOCAP1, GOLPH1, PAP7 ENSG00000182827 Acyl-CoA binding domain containing 3 1 226144679-226186730 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA015594 Uncertain Supportive Golgi apparatus Expressed in all thyroid gland: 26.7 ACN9 DC11 ENSG00000196636 ACN9 homolog (S. cerevisiae) 7 97116590-97181763 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA020523 Uncertain Uncertain Mitochondria, Cytoskeleton (Microtubules) Expressed in all kidney: 10.6 ACO2 ACONM ENSG00000100412 Aconitase 2, mitochondrial 22 41469125-41528989 Citric acid cycle related proteins, Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA001097 Supportive Supportive Mitochondria, Nucleus Expressed in all heart muscle: 247.5 ACOT2 Mte1, ZAP128 ENSG00000119673 Acyl-CoA thioesterase 2 14 73567620-73575658 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA043705 Uncertain Uncertain Mitochondria Expressed in all liver: 57.3 ACOT7 ACH1, ACT, BACH, CTE-II, hBACH, LACH1, MGC1126 ENSG00000097021 Acyl-CoA thioesterase 7 1 6264269-6394391 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA025735, HPA025762 Supportive Supportive Cytoplasm, Nucleus but not nucleoli Mixed cerebral cortex: 56.2 ACOT9 ACATE2, CGI-16, MT-ACT48 ENSG00000123130 Acyl-CoA thioesterase 9 X 23702253-23766475 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA035533 Supportive Uncertain Plasma membrane, Cytoplasm, Nucleus but not nucleoli Expressed in all smooth muscle: 27.7 ACSF2 ACSMW, FLJ20920 ENSG00000167107 Acyl-CoA synthetase family member 2 17 50426158-50474845 Mitochondrial proteins, Predicted membrane proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA024693 Uncertain Uncertain Nucleus but not nucleoli, Cytoplasm, Cytoskeleton (Microtubules) Expressed in all kidney: 114.1 ACSF3 ENSG00000176715 Acyl-CoA synthetase family member 3 16 89088375-89155846 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA008322, HPA008323 Supportive Expressed in all duodenum: 19.9 ACSL1 ACS1, FACL1, FACL2, LACS, LACS1, LACS2 ENSG00000151726 Acyl-CoA synthetase long-chain family member 1 4 184755595-184826818 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA011316, HPA011964 Uncertain Supportive Nucleus, Mitochondria Expressed in all adipose tissue: 567.2 ACSL3 ACS3, FACL3, PRO2194 ENSG00000123983 Acyl-CoA synthetase long-chain family member 3 2 222860934-222944639 Cancer-related genes, Enzymes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA011315 Uncertain Expressed in all prostate: 106.3 ACSL4 ACS4, FACL4, LACS4, MRX63, MRX68 ENSG00000068366 Acyl-CoA synthetase long-chain family member 4 X 109624244-109733403 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA000286, HPA005552 Supportive Supportive Golgi apparatus, Mitochondria Expressed in all appendix: 35.1 ACSL5 ACS2, ACS5, FACL5 ENSG00000197142 Acyl-CoA synthetase long-chain family member 5 10 112374018-112428380 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA007162, CAB062546 Supportive Supportive Mitochondria, Nucleus, Nucleoli Expressed in all small intestine: 322.8 ACSL6 ACS2, FACL6, KIAA0837, LACS2, LACS5 ENSG00000164398 Acyl-CoA synthetase long-chain family member 6 5 131806990-132012243 Cancer-related genes, Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA040470 Uncertain Group enriched 6 bone marrow: 13.8;cerebral cortex: 31.6;testis: 30.3 duodenum: 4.5 ACSM1 BUCS1, MACS1 ENSG00000166743 Acyl-CoA synthetase medium-chain family member 1 16 20623237-20698890 Enzymes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at transcript level Evidence at transcript level Evidence at transcript level HPA046291 Uncertain Tissue enhanced 0 liver: 3.8;prostate: 4.4 testis: 1.9 ACSM2A A-923A4.1, ACSM2, MGC150530 ENSG00000183747 Acyl-CoA synthetase medium-chain family member 2A 16 20451461-20487667 Enzymes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA057699 Supportive Group enriched 892 kidney: 189.3;liver: 103.8 adipose tissue: 0.1 ACSM2B ACSM2, HXMA, HYST1046 ENSG00000066813 Acyl-CoA synthetase medium-chain family member 2B 16 20536226-20576427 Enzymes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA057699 Supportive Group enriched 171 kidney: 236.9;liver: 137.6 lung: 1.0 ACSM3 SA, SAH ENSG00000005187 Acyl-CoA synthetase medium-chain family member 3 16 20610243-20797581 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA041013 Uncertain Tissue enhanced 0 liver: 48.5 ovary: 44.9 ACSM4 ENSG00000215009 Acyl-CoA synthetase medium-chain family member 4 12 7304284-7328724 Enzymes, Mitochondrial proteins, Predicted membrane proteins Evidence at transcript level Evidence at transcript level Evidence at transcript level HPA049895 Uncertain Tissue enriched 7 testis: 0.7 adipose tissue: 0.0 ACSM5 FLJ20581 ENSG00000183549 Acyl-CoA synthetase medium-chain family member 5 16 20409534-20441336 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA041435 Uncertain Tissue enhanced 0 liver: 83.7 adipose tissue: 17.3 ACSM6 bA310E22.3, C10orf129 ENSG00000173124 Acyl-CoA synthetase medium-chain family member 6 10 95194200-95228928 Enzymes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA044593 Uncertain Tissue enhanced 0 stomach: 0.6 pancreas: 0.3 ACSS1 ACAS2L, AceCS2L, dJ568C11.3, MGC33843 ENSG00000154930 Acyl-CoA synthetase short-chain family member 1 20 25006230-25058980 Enzymes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041014, HPA043228 Supportive Expressed in all placenta: 101.7 ACSS3 FLJ21963 ENSG00000111058 Acyl-CoA synthetase short-chain family member 3 12 80936414-81261205 Enzymes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA039353, HPA047956, HPA061517 Uncertain Uncertain Mitochondria Mixed liver: 18.8 ADCK3 CABC1, COQ8, SCAR9 ENSG00000163050 AarF domain containing kinase 3 1 226897536-226987545 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA061662 Supportive Mitochondria Tissue enriched 7 skeletal muscle: 294.5 adipose tissue: 43.2 ADHFE1 ADHFe1, FLJ32430 ENSG00000147576 Alcohol dehydrogenase, iron containing, 1 8 66430185-66471601 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA023062 Uncertain Uncertain Vesicles Tissue enhanced 0 heart muscle: 11.8 liver: 9.0 AFG3L2 SCA28, SPAX5 ENSG00000141385 AFG3-like AAA ATPase 2 18 12328944-12377314 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA004479, HPA004480 Supportive Supportive Mitochondria Expressed in all duodenum: 61.7 AGK FLJ10842, MULK ENSG00000006530 Acylglycerol kinase 7 141551189-141655244 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA020959, HPA053471 Supportive Supportive Mitochondria, Vesicles Expressed in all heart muscle: 14.9 AGMAT FLJ23384 ENSG00000116771 Agmatine ureohydrolase (agmatinase) 1 15572353-15585110 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA026443, HPA028321 Supportive Tissue enhanced 0 kidney: 122.6 liver: 31.9 AGXT AGT, AGT1, AGXT1, PH1, SPAT, SPT ENSG00000172482 Alanine-glyoxylate aminotransferase 2 240868479-240880502 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA035370, HPA035371 Supportive Supportive Vesicles Tissue enriched 47 liver: 424.6 kidney: 9.0 AGXT2 AGT2 ENSG00000113492 Alanine--glyoxylate aminotransferase 2 5 34998101-35048135 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA037382 Uncertain Group enriched 24 kidney: 99.4;liver: 33.9 small intestine: 2.7 AIFM1 AIF, CMTX4, NAMSD, PDCD8 ENSG00000156709 Apoptosis-inducing factor, mitochondrion-associated, 1 X 130129362-130165887 Disease related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB003764, HPA030611 Supportive Expressed in all kidney: 93.8 AIFM2 AMID, FLJ14497, PRG3 ENSG00000042286 Apoptosis-inducing factor, mitochondrion-associated, 2 10 70098223-70132934 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA042309 Uncertain Expressed in all adipose tissue: 26.9 AIFM3 AIFL, FLJ30473 ENSG00000183773 Apoptosis-inducing factor, mitochondrion-associated, 3 22 20965108-20981360 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA001271 Uncertain Tissue enhanced 0 cerebral cortex: 8.4;colon: 11.5 rectum: 5.4 AK2 ENSG00000004455 Adenylate kinase 2 1 33007984-33080996 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA018479 Uncertain Expressed in all kidney: 88.2 AK3 AK3L1, AK6, AKL3L1 ENSG00000147853 Adenylate kinase 3 9 4709559-4742043 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA063324 Uncertain Expressed in all liver: 73.0 AK4 AK3, AK3L1 ENSG00000162433 Adenylate kinase 4 1 65147549-65232145 Enzymes, Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA042753, HPA049461 Supportive Supportive Mitochondria Tissue enhanced 0 kidney: 86.2 liver: 28.1 AKAP1 AKAP121, AKAP149, AKAP84, D-AKAP1, PPP1R43, PRKA1, S-AKAP84, SAKAP84, TDRD17 ENSG00000121057 A kinase (PRKA) anchor protein 1 17 57085092-57121349 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA008620, HPA008691, CAB019286 Supportive Supportive Mitochondria Expressed in all testis: 78.6 AKAP10 D-AKAP2, MGC9414, PRKA10 ENSG00000108599 A kinase (PRKA) anchor protein 10 17 19904302-19978343 Disease related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA028901 Uncertain Supportive Plasma membrane, Cytoplasm Expressed in all thyroid gland: 14.4 ALAS1 ALAS, ALAS3 ENSG00000023330 Aminolevulinate, delta-, synthase 1 3 52198086-52214327 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB017498, HPA035860 Supportive Supportive Mitochondria, Nucleus Expressed in all adrenal gland: 475.2 ALAS2 ASB ENSG00000158578 Aminolevulinate, delta-, synthase 2 X 55009055-55031064 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA001638 Uncertain Tissue enriched 18 bone marrow: 298.7 placenta: 16.5 ALDH18A1 GSAS, P5CS, PYCS ENSG00000059573 Aldehyde dehydrogenase 18 family, member A1 10 95605929-95656706 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA008333, HPA012604 Supportive Supportive Mitochondria Expressed in all duodenum: 65.5 ALDH1B1 ALDH5, ALDHX ENSG00000137124 Aldehyde dehydrogenase 1 family, member B1 9 38392664-38398661 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA021037 Uncertain Supportive Mitochondria, Nucleus but not nucleoli, Vesicles Expressed in all smooth muscle: 106.6 ALDH2 ENSG00000111275 Aldehyde dehydrogenase 2 family (mitochondrial) 12 111766887-111809985 Cancer-related genes, Enzymes, FDA approved drug targets, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA051065 Uncertain Expressed in all liver: 715.6 ALDH4A1 ALDH4, P5CDh ENSG00000159423 Aldehyde dehydrogenase 4 family, member A1 1 18871430-18902781 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB004645, HPA006401 Supportive Uncertain Cytoplasm Expressed in all kidney: 176.5 ALDH5A1 SSADH, SSDH ENSG00000112294 Aldehyde dehydrogenase 5 family, member A1 6 24494852-24537207 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA029715, HPA029716 Supportive Supportive Mitochondria Expressed in all liver: 33.5 ALDH6A1 MMSDH ENSG00000119711 Aldehyde dehydrogenase 6 family, member A1 14 74056850-74084493 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA029072, HPA029073, HPA029074, HPA029075 Supportive Supportive Mitochondria Group enriched 5 kidney: 257.6;liver: 120.0 cerebral cortex: 36.5 AMACR RACE ENSG00000242110 Alpha-methylacyl-CoA racemase 5 33986178-34008108 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB001809, HPA019527, HPA020912 Supportive Uncertain Plasma membrane, Vesicles Expressed in all kidney: 80.3 AMT GCST, NKH ENSG00000145020 Aminomethyltransferase 3 49416778-49422753 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA005566 Supportive Expressed in all liver: 12.2 APEX2 APE2, APEXL2, XTH2, ZGRF2 ENSG00000169188 APEX nuclease (apurinic/apyrimidinic endonuclease) 2 X 55000357-55009057 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA030872, HPA048577 Uncertain Supportive Nucleus, Nucleoli, Vesicles Expressed in all tonsil: 10.7 APOO FAM121B, MGC4825, My025 ENSG00000184831 Apolipoprotein O X 23833353-23907934 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA003187 Supportive Uncertain Mitochondria, Cytoplasm Expressed in all heart muscle: 28.0 ARG2 ENSG00000081181 Arginase 2 14 67619798-67651720 Cancer-related genes, Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA000663, CAB009435 Supportive Supportive Mitochondria, Nucleus but not nucleoli Group enriched 6 kidney: 28.1;prostate: 79.7;thyroid gland: 104.7 small intestine: 11.3 ARL2BP BART, BART1, RP66 ENSG00000102931 ADP-ribosylation factor-like 2 binding protein 16 57245098-57253635 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA043066, HPA048440 Uncertain Supportive Nucleus but not nucleoli, Cytoplasm, Golgi apparatus Expressed in all testis: 49.2 ARMS2 ARMD8, LOC387715 ENSG00000254636 Age-related maculopathy susceptibility 2 10 122454653-122457352 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at transcript level Evidence at transcript level Evidence at transcript level Tissue enhanced 0 placenta: 1.2;testis: 1.2 ovary: 0.3 ATP5A1 ATP5A, ATP5AL2, ATPM, hATP1, OMR, ORM ENSG00000152234 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle 18 46080248-46104334 Disease related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB013067, HPA040622, HPA044202 Supportive Supportive Mitochondria Expressed in all heart muscle: 684.5 ATP5B ATPSB ENSG00000110955 ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide 12 56638175-56646068 Cancer-related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA001520, HPA001528, CAB017527 Supportive Supportive Mitochondria Expressed in all heart muscle: 1043.8 ATP5C1 ATP5C, ATP5CL1 ENSG00000165629 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1 10 7788129-7807815 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA060949 Uncertain Expressed in all heart muscle: 374.1 ATP5D ENSG00000099624 ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit 19 1241746-1244826 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA002865 Uncertain Expressed in all skeletal muscle: 162.1 ATP5E ENSG00000124172 ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit 20 59025467-59032382 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA042142 Uncertain Expressed in all appendix: 36.8 ATP5F1 ENSG00000116459 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1 1 111448864-111462773 Mitochondrial proteins, Predicted membrane proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA046067, HPA057347 Supportive Supportive Nucleus but not nucleoli, Mitochondria Expressed in all heart muscle: 27.6 ATP5G1 ATP5G ENSG00000159199 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9) 17 48892765-48895871 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at transcript level Evidence at transcript level Evidence at transcript level Expressed in all heart muscle: 342.4 ATP5G2 ENSG00000135390 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9) 12 53632726-53677408 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at transcript level Evidence at transcript level Evidence at transcript level HPA051469 Uncertain Expressed in all fallopian tube: 440.8 ATP5G3 ENSG00000154518 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9) 2 175176258-175184607 Mitochondrial proteins, Predicted membrane proteins Evidence at transcript level Evidence at transcript level Evidence at transcript level Expressed in all heart muscle: 471.3 ATP5H ATP5JD, ATPQ ENSG00000167863 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d 17 75038863-75046985 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA042777, HPA048459 Supportive Supportive Mitochondria, Nucleus but not nucleoli Expressed in all heart muscle: 432.6 ATP5I ENSG00000169020 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E 4 672436-674338 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA035010 Supportive Supportive Mitochondria Expressed in all heart muscle: 481.6 ATP5J ATP5, ATP5A, ATPM, CF6 ENSG00000154723 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6 21 25716503-25735673 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA031069 Supportive Supportive Mitochondria Expressed in all heart muscle: 454.5 ATP5J2 ATP5JL, F1Fo-ATPase ENSG00000241468 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2 7 99448475-99466331 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA067267 Supportive Mitochondria, Nucleus but not nucleoli Expressed in all heart muscle: 640.6 ATP5L ATP5JG ENSG00000167283 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G 11 118401154-118431496 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA044629 Uncertain Supportive Mitochondria Expressed in all heart muscle: 80.4 ATP5O ATPO, OSCP ENSG00000241837 ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit 21 33903453-33915980 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB016209, HPA041394 Supportive Supportive Mitochondria Expressed in all heart muscle: 445.2 ATP5S ATPW, HSU79253 ENSG00000125375 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit s (factor B) 14 50312326-50335558 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA046967, HPA062690 Uncertain Uncertain Nucleus but not nucleoli, Mitochondria Mixed fallopian tube: 5.7 ATP7B WND ENSG00000123191 ATPase, Cu++ transporting, beta polypeptide 13 51932673-52011494 Cancer-related genes, Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA013187 Supportive Mixed testis: 9.2 ATPAF1 ATP11, Atp11p, FLJ22351 ENSG00000123472 ATP synthase mitochondrial F1 complex assembly factor 1 1 46632737-46673867 Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA028382, HPA044950 Uncertain Uncertain Mitochondria Expressed in all heart muscle: 124.0 ATPAF2 ATP12, Atp12p, LP3663, MGC29736 ENSG00000171953 ATP synthase mitochondrial F1 complex assembly factor 2 17 17977409-18039209 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA023329, HPA059422 Supportive Supportive Cytoplasm Expressed in all tonsil: 11.7 ATPIF1 ATPI, ATPIP, IP, MGC1167, MGC8898 ENSG00000130770 ATPase inhibitory factor 1 1 28236109-28246906 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA027999 Supportive Supportive Mitochondria Expressed in all heart muscle: 341.0 AUH ENSG00000148090 AU RNA binding protein/enoyl-CoA hydratase 9 91213815-91361913 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA004171 Supportive Expressed in all kidney: 49.1 BAD BBC2, BCL2L8 ENSG00000002330 BCL2-associated agonist of cell death 11 64269830-64284704 Cancer-related genes, Mitochondrial proteins, Predicted intracellular proteins, RAS pathway related proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB004205, HPA028185, HPA062105 Supportive Supportive Mitochondria Expressed in all stomach: 37.0 BAX BCL2L4 ENSG00000087088 BCL2-associated X protein 19 48954815-48961798 Cancer-related genes, Mitochondrial proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB004206, HPA027878 Supportive Expressed in all rectum: 65.8 BBC3 JFY1, PUMA ENSG00000105327 BCL2 binding component 3 19 47220822-47232766 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB007752 Uncertain Mixed colon: 4.3 BCAT2 BCAM, BCT2 ENSG00000105552 Branched chain amino-acid transaminase 2, mitochondrial 19 48795062-48811029 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA054091 Supportive Expressed in all urinary bladder: 39.0 BCKDHA MSU, OVD1A ENSG00000248098 Branched chain keto acid dehydrogenase E1, alpha polypeptide 19 41397460-41431345 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA036640 Supportive Expressed in all esophagus: 39.5 BCKDHB ENSG00000083123 Branched chain keto acid dehydrogenase E1, beta polypeptide 6 80106647-80346270 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted secreted proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA031580 Uncertain Expressed in all liver: 29.7 BCKDK ENSG00000103507 Branched chain ketoacid dehydrogenase kinase 16 31106107-31112791 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA017995, HPA056067 Supportive Supportive Mitochondria Expressed in all heart muscle: 20.6 BCL2 Bcl-2, PPP1R50 ENSG00000171791 B-cell CLL/lymphoma 2 18 63123346-63320128 Cancer-related genes, Disease related genes, FDA approved drug targets, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB000003 Uncertain Expressed in all thyroid gland: 41.1 BCL2L1 Bcl-X, bcl-xL, bcl-xS, BCL2L, BCLX, PPP1R52 ENSG00000171552 BCL2-like 1 20 31664452-31723989 Cancer-related genes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins, RAS pathway related proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB000105, HPA035734, CAB072801, CAB072802 Uncertain Supportive Mitochondria, Vesicles Expressed in all bone marrow: 68.3 BCL2L10 BCL-B, Boo, Diva ENSG00000137875 BCL2-like 10 (apoptosis facilitator) 15 52109263-52112775 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level HPA042222 Uncertain Tissue enhanced 0 skin: 3.4 liver: 2.6 BCL2L13 BCL-RAMBO, MIL1 ENSG00000099968 BCL2-like 13 (apoptosis facilitator) 22 17628855-17730855 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB002052, HPA030994, HPA050377 Uncertain Uncertain Mitochondria, Cytoplasm Expressed in all testis: 16.0 BCL2L2 BCL-W, KIAA0271, PPP1R51 ENSG00000129473 BCL2-like 2 14 23298790-23311759 Cancer-related genes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level CAB040539 Uncertain Expressed in all cerebral cortex: 42.0 BCL2L2-PABPN1 ENSG00000258643 BCL2L2-PABPN1 readthrough 14 23306835-23325369 Cancer-related genes, Mitochondrial proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level HPA000637 Uncertain Mixed testis: 10.2 BCS1L BCS, BJS, h-BCS, Hs.6719 ENSG00000074582 BC1 (ubiquinol-cytochrome c reductase) synthesis-like 2 218658764-218663443 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA037700, HPA037701 Supportive Uncertain Vesicles Expressed in all fallopian tube: 20.0 BDH1 BDH, SDR9C1 ENSG00000161267 3-hydroxybutyrate dehydrogenase, type 1 3 197509783-197573323 Candidate cardiovascular disease genes, Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA030947, HPA058709 Supportive Supportive Mitochondria, Nucleus but not nucleoli Expressed in all liver: 123.1 BID ENSG00000015475 BH3 interacting domain death agonist 22 17734138-17774770 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA000722, CAB003771 Supportive Supportive Cytoplasm Expressed in all bone marrow: 42.9 BLID BRCC2 ENSG00000259571 BH3-like motif containing, cell death inducer 11 122115354-122116215 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level No evidence Evidence at protein level Not detected adipose tissue: 0.0 BNIP3 Nip3 ENSG00000176171 BCL2/adenovirus E1B 19kDa interacting protein 3 10 131966455-131981931 Cancer-related genes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA003015, CAB011676 Supportive Uncertain Cytoplasm Expressed in all pancreas: 36.0 BNIP3L BNIP3a, Nix ENSG00000104765 BCL2/adenovirus E1B 19kDa interacting protein 3-like 8 26382898-26505636 Cancer-related genes, Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA015652, CAB025371 Supportive Supportive Mitochondria, Nucleus but not nucleoli Expressed in all ovary: 100.8 BZRAP1 KIAA0612, PRAX-1, RIM-BP1, RIMBP1 ENSG00000005379 Benzodiazepine receptor (peripheral) associated protein 1 17 58301228-58328760 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA024662, HPA025244 Supportive Uncertain Nucleoli, Mitochondria Expressed in all fallopian tube: 33.2 C10orf2 FLJ21832, IOSCA, PEO, PEO1, TWINKLE, TWINL ENSG00000107815 Chromosome 10 open reading frame 2 10 100987367-100994401 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA002532 Uncertain Expressed in all testis: 7.5 C14orf159 FLJ39975 ENSG00000133943 Chromosome 14 open reading frame 159 14 91060333-91225632 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041423, HPA052932 Uncertain Supportive Cytoplasm Expressed in all heart muscle: 68.1 C14orf2 MP68 ENSG00000156411 Chromosome 14 open reading frame 2 14 103912288-103928269 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA058978, HPA060520 Supportive Supportive Mitochondria, Nucleoli Expressed in all heart muscle: 173.1 C15orf62 LOC643338 ENSG00000188277 Chromosome 15 open reading frame 62 15 40770080-40772449 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at transcript level HPA044636 Uncertain Group enriched 5 esophagus: 11.0;skin: 7.3;tonsil: 5.5 lymph node: 1.5 C1QBP gC1Q-R, gC1qR, HABP1, p32, SF2p32 ENSG00000108561 Complement component 1, q subcomponent binding protein 17 5432777-5448830 Cancer-related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA026483 Supportive Uncertain Plasma membrane, Mitochondria Expressed in all rectum: 121.1 C21orf33 D21S2048E, ES1, GT335, HES1, KNP-I, KNP-Ia, KNPH, KNPI ENSG00000160221 Chromosome 21 open reading frame 33 21 44133605-44145723 Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA018517 Supportive Supportive Mitochondria, Nucleus Expressed in all kidney: 68.3 C2orf47 DKFZp666A212, FLJ22555 ENSG00000162972 Chromosome 2 open reading frame 47 2 199955317-200008540 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA064013 Uncertain Mitochondria Expressed in all kidney: 20.0 CA5A CA5, CAV, CAVA ENSG00000174990 Carbonic anhydrase VA, mitochondrial 16 87881546-87936529 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Tissue enriched 6 liver: 0.6 adipose tissue: 0.0 CA5B ENSG00000169239 Carbonic anhydrase VB, mitochondrial X 15688830-15787624 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA012618 Uncertain Supportive Mitochondria, Nucleus Mixed testis: 10.9 CAPRIN2 C1QDC1, caprin-2, EEG1, FLJ11391, FLJ22569, RNG140 ENSG00000110888 Caprin family member 2 12 30709552-30754951 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA039746 Uncertain Supportive Cytoplasm, Nucleus, Centrosome Tissue enhanced 0 testis: 16.2 cerebral cortex: 7.5 CARS2 FLJ12118 ENSG00000134905 Cysteinyl-tRNA synthetase 2, mitochondrial (putative) 13 110641412-110713603 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041776, HPA043935 Uncertain Uncertain Nucleus but not nucleoli, Mitochondria Expressed in all adrenal gland: 16.6 CASQ1 CASQ, PDIB1 ENSG00000143318 Calsequestrin 1 (fast-twitch, skeletal muscle) 1 160190556-160201886 Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA007845, CAB015170, HPA026823 Supportive Tissue enriched 31 skeletal muscle: 1163.8 esophagus: 36.9 CCDC90B MDS011, MDS025 ENSG00000137500 Coiled-coil domain containing 90B 11 83259097-83286407 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA011130, HPA011931 Supportive Supportive Mitochondria Expressed in all testis: 49.7 CDS2 ENSG00000101290 CDP-diacylglycerol synthase (phosphatidate cytidylyltransferase) 2 20 5126786-5197887 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA019698 Uncertain Uncertain Endoplasmic reticulum, Cytoplasm Expressed in all cerebral cortex: 25.4 CECR5 ENSG00000069998 Cat eye syndrome chromosome region, candidate 5 22 17137511-17165287 Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA005548 Uncertain Uncertain Mitochondria Expressed in all heart muscle: 17.8 CEP89 CCDC123, FLJ14640 ENSG00000121289 Centrosomal protein 89kDa 19 32878996-32971991 Cancer-related genes, Disease related genes, Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA039382, HPA040056 Uncertain Supportive Cytoplasm, Plasma membrane Expressed in all fallopian tube: 11.0 CHCHD10 C22orf16, N27C7-4 ENSG00000250479 Coiled-coil-helix-coiled-coil-helix domain containing 10 22 23765834-23768443 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA003440 Uncertain Supportive Mitochondria Expressed in all heart muscle: 441.6 CHCHD2 C7orf17 ENSG00000106153 Coiled-coil-helix-coiled-coil-helix domain containing 2 7 56101569-56106576 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA027407, HPA052510 Uncertain Supportive Mitochondria Expressed in all adrenal gland: 194.0 CHCHD3 FLJ20420, MINOS3, PPP1R22 ENSG00000106554 Coiled-coil-helix-coiled-coil-helix domain containing 3 7 132784868-133082088 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA042935 Supportive Supportive Mitochondria Expressed in all skeletal muscle: 48.7 CHCHD4 FLJ31709, MIA40, TIMM40 ENSG00000163528 Coiled-coil-helix-coiled-coil-helix domain containing 4 3 14112077-14124870 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA034688, HPA063727 Uncertain Supportive Mitochondria Expressed in all rectum: 13.4 CHDH ENSG00000016391 Choline dehydrogenase 3 53812335-53846390 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA036633, HPA058130 Supportive Tissue enhanced 0 kidney: 28.4 small intestine: 8.6 CISD1 C10orf70, MDS029, mitoNEET, ZCD1 ENSG00000122873 CDGSH iron sulfur domain 1 10 58269058-58289586 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB045965, HPA074383 Uncertain Supportive Mitochondria Mixed heart muscle: 19.8 CISD3 Miner2 ENSG00000277972 CDGSH iron sulfur domain 3 17 38730235-38735044 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level HPA053436, HPA054400 Uncertain Expressed in all duodenum: 12.3 CKMT1A CKMT1 ENSG00000223572 Creatine kinase, mitochondrial 1A 15 43692886-43699222 Enzymes, FDA approved drug targets, Mitochondrial proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level HPA043491 Uncertain Mixed colon: 43.8 CKMT1B CKMT, CKMT1, UMTCK ENSG00000237289 Creatine kinase, mitochondrial 1B 15 43593054-43604901 Enzymes, FDA approved drug targets, Mitochondrial proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level HPA043491 Uncertain Tissue enhanced 0 colon: 33.5 rectum: 27.3 CKMT2 SMTCK ENSG00000131730 Creatine kinase, mitochondrial 2 (sarcomeric) 5 81233285-81266397 Enzymes, FDA approved drug targets, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA051880 Uncertain Group enriched 27 heart muscle: 628.6;skeletal muscle: 398.9 prostate: 19.3 CLPP ENSG00000125656 Caseinolytic mitochondrial matrix peptidase proteolytic subunit 19 6361452-6368908 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA010649 Supportive Supportive Mitochondria Expressed in all skeletal muscle: 31.3 CLPX ENSG00000166855 Caseinolytic mitochondrial matrix peptidase chaperone subunit 15 65148219-65185342 Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA040262, HPA048199 Uncertain Supportive Mitochondria Expressed in all liver: 13.6 CLYBL CLB ENSG00000125246 Citrate lyase beta like 13 99606669-99897134 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA039959, HPA040691 Supportive Uncertain Cytoplasm, Cytoskeleton (Intermediate filaments) Expressed in all kidney: 37.1 CMC1 C3orf68, MGC61571 ENSG00000187118 C-x(9)-C motif containing 1 3 28241584-28325142 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA043333 Uncertain Expressed in all kidney: 32.7 CMC4 MTCP1, MTCP1NB, p8, P8MTCP1 ENSG00000182712 C-x(9)-C motif containing 4 X 155061622-155071362 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA045866 Uncertain Supportive Mitochondria Expressed in all heart muscle: 16.4 CMPK2 TYKi, UMP-CMPK2 ENSG00000134326 Cytidine monophosphate (UMP-CMP) kinase 2, mitochondrial 2 6840570-6866635 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041430 Uncertain Supportive Nucleus but not nucleoli, Mitochondria Mixed salivary gland: 4.9 COQ10A FLJ32452 ENSG00000135469 Coenzyme Q10 homolog A (S. cerevisiae) 12 56266858-56270966 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA068931 Uncertain Cytoplasm, Endoplasmic reticulum, Golgi apparatus Expressed in all skeletal muscle: 73.2 COQ10B FLJ13448 ENSG00000115520 Coenzyme Q10 homolog B (S. cerevisiae) 2 197453423-197475308 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA046057 Uncertain Uncertain Cytoplasm Expressed in all adrenal gland: 34.0 COQ2 CL640, FLJ26072 ENSG00000173085 Coenzyme Q2 4-hydroxybenzoate polyprenyltransferase 4 83261536-83284914 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level HPA056599, HPA068727 Uncertain Uncertain Cytoplasm Expressed in all adrenal gland: 14.5 COQ3 bA9819.1 ENSG00000132423 Coenzyme Q3 methyltransferase 6 99369400-99394204 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA031273, HPA031274 Supportive Uncertain Nucleus but not nucleoli, Mitochondria Expressed in all heart muscle: 15.2 COQ5 MGC4767 ENSG00000110871 Coenzyme Q5 homolog, methyltransferase (S. cerevisiae) 12 120503274-120534434 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA049487 Uncertain Uncertain Nucleoli, Mitochondria Expressed in all skeletal muscle: 25.8 COQ6 CGI-10 ENSG00000119723 Coenzyme Q6 monooxygenase 14 73949926-73963670 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA051371 Uncertain Expressed in all adrenal gland: 22.4 COQ9 C16orf49, DKFZP434K046 ENSG00000088682 Coenzyme Q9 16 57447425-57461275 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA040918 Supportive Uncertain Cytoplasm Expressed in all heart muscle: 66.4 COX10 ENSG00000006695 Cytochrome c oxidase assembly homolog 10 (yeast) 17 14069496-14208677 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA032005, HPA032006 Supportive Uncertain Nucleoli, Mitochondria, Cytoplasm Expressed in all testis: 23.0 COX11 COX11P ENSG00000166260 Cytochrome c oxidase assembly homolog 11 (yeast) 17 54951902-54968785 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA044020 Uncertain Expressed in all duodenum: 41.5 COX15 ENSG00000014919 Cytochrome c oxidase assembly homolog 15 (yeast) 10 99711844-99732100 Disease related genes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA037727, HPA037728, HPA066096 Uncertain Supportive Mitochondria, Nucleus Expressed in all adrenal gland: 22.4 COX16 C14orf112, HSPC203 ENSG00000133983 COX16 cytochrome c oxidase assembly homolog (S. cerevisiae) 14 70325081-70359731 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA062659 Uncertain Expressed in all thyroid gland: 20.9 COX17 ENSG00000138495 COX17 cytochrome c oxidase copper chaperone 3 119654513-119677454 Cancer-related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA042226, HPA048158 Supportive Supportive Mitochondria Expressed in all adrenal gland: 20.5 COX18 FLJ38991 ENSG00000163626 COX18 cytochrome C oxidase assembly factor 4 73056080-73069755 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA046772, HPA049489 Uncertain Expressed in all kidney: 8.0 COX4I1 COX4, COX4-1 ENSG00000131143 Cytochrome c oxidase subunit IV isoform 1 16 85798633-85807044 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA002485, CAB004080 Supportive Supportive Nucleus, Mitochondria Expressed in all heart muscle: 936.3 COX4I2 COX4-2, COX4B, COX4L2, COXIV-2, dJ857M17.2 ENSG00000131055 Cytochrome c oxidase subunit IV isoform 2 (lung) 20 31637888-31645006 Disease related genes, Mitochondrial proteins, Potential drug targets, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA029307 Uncertain Tissue enhanced 0 placenta: 70.1 lung: 23.3 COX5A ENSG00000178741 Cytochrome c oxidase subunit Va 15 74919791-74938168 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA027526 Supportive Expressed in all skeletal muscle: 414.5 COX5B ENSG00000135940 Cytochrome c oxidase subunit Vb 2 97646040-97648383 Mitochondrial proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA034517 Supportive Supportive Mitochondria Expressed in all skeletal muscle: 357.4 COX6A1 COX6A ENSG00000111775 Cytochrome c oxidase subunit VIa polypeptide 1 12 120438090-120440742 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA062394 Uncertain Expressed in all colon: 143.6 COX6A2 ENSG00000156885 Cytochrome c oxidase subunit VIa polypeptide 2 16 31427731-31428428 Mitochondrial proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level Group enriched 18 heart muscle: 646.0;skeletal muscle: 1472.4 prostate: 59.2 COX6B1 COX6B, COXG ENSG00000126267 Cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) 19 35648223-35658861 Disease related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA004192 Supportive Supportive Mitochondria Expressed in all heart muscle: 404.4 COX6B2 COXVIB2, CT59, FLJ32865 ENSG00000160471 Cytochrome c oxidase subunit VIb polypeptide 2 (testis) 19 55349306-55354814 Mitochondrial proteins, Predicted intracellular proteins, Transporters Evidence at transcript level Evidence at transcript level Evidence at transcript level HPA035014 Uncertain Nucleus but not nucleoli, Plasma membrane, Cytoplasm Tissue enriched 12 testis: 42.6 rectum: 3.6 COX6C ENSG00000164919 Cytochrome c oxidase subunit VIc 8 99873200-99894062 Cancer-related genes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA014295, CAB016244 Supportive Supportive Mitochondria Expressed in all skeletal muscle: 171.9 COX7A1 COX7A, COX7AH ENSG00000161281 Cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) 19 36150922-36152869 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Group enriched 6 heart muscle: 327.9;skeletal muscle: 664.4 adipose tissue: 79.8 COX7A2 COX7AL, COXVIIa-L ENSG00000112695 Cytochrome c oxidase subunit VIIa polypeptide 2 (liver) 6 75237675-75250323 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Expressed in all rectum: 397.9 COX7A2L COX7AR, COX7RP, EB1, SIG81 ENSG00000115944 Cytochrome c oxidase subunit VIIa polypeptide 2 like 2 42333546-42425088 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA059124, CAB073545 Supportive Mitochondria, Nucleoli Expressed in all adrenal gland: 167.5 COX7B ENSG00000131174 Cytochrome c oxidase subunit VIIb X 77899438-77907373 Disease related genes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA058041 Uncertain Expressed in all heart muscle: 56.2 COX7B2 ENSG00000170516 Cytochrome c oxidase subunit VIIb2 4 46734827-46909235 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at transcript level Evidence at transcript level Evidence at transcript level Tissue enriched 50 testis: 71.7 placenta: 1.4 COX7C ENSG00000127184 Cytochrome c oxidase subunit VIIc 5 86617904-86620962 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA046647 Uncertain Expressed in all heart muscle: 347.7 COX8A COX, COX8, COX8-2, COX8L, VIII, VIII-L ENSG00000176340 Cytochrome c oxidase subunit VIIIA (ubiquitous) 11 63974607-63976543 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA055942 Supportive Expressed in all skeletal muscle: 402.1 COX8C COX8-3 ENSG00000187581 Cytochrome c oxidase subunit VIIIC 14 93347191-93348356 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at transcript level Evidence at transcript level Evidence at transcript level HPA003127 Uncertain Tissue enriched 98 testis: 21.9 fallopian tube: 0.2 CPOX CPO, CPX, HCP ENSG00000080819 Coproporphyrinogen oxidase 3 98521132-98593723 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA015736, HPA054448 Uncertain Supportive Mitochondria Expressed in all bone marrow: 21.6 CPS1 ENSG00000021826 Carbamoyl-phosphate synthase 1, mitochondrial 2 210477682-210679107 Disease related genes, Enzymes, FDA approved drug targets, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB003781, HPA021400 Supportive Uncertain Nucleoli Group enriched 33 duodenum: 166.9;liver: 441.1;small intestine: 99.4 testis: 7.0 CPT1A CPT1, CPT1-L, L-CPT1 ENSG00000110090 Carnitine palmitoyltransferase 1A (liver) 11 68754620-68844410 Disease related genes, Enzymes, FDA approved drug targets, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA008835 Supportive Supportive Mitochondria Expressed in all colon: 56.9 CPT1B CPT1-M, M-CPT1 ENSG00000205560 Carnitine palmitoyltransferase 1B (muscle) 22 50568861-50578465 Enzymes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA029583 Uncertain Expressed in all heart muscle: 87.4 CPT1C CPT1P, CPTIC, FLJ23809 ENSG00000169169 Carnitine palmitoyltransferase 1C 19 49690898-49713731 Enzymes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA014529 Uncertain Tissue enhanced 0 cerebral cortex: 16.6 gallbladder: 5.1 CPT2 CPT1, CPTASE ENSG00000157184 Carnitine palmitoyltransferase 2 1 53196429-53214197 Disease related genes, Enzymes, FDA approved drug targets, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA028201, HPA028202, HPA028214 Supportive Supportive Nucleoli, Nucleus but not nucleoli, Mitochondria Expressed in all liver: 25.5 CRAT CAT1 ENSG00000095321 Carnitine O-acetyltransferase 9 129094810-129111189 Enzymes, Mitochondrial proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA019230, HPA020260, HPA022815 Supportive Uncertain Nucleus but not nucleoli, Nuclear membrane Expressed in all testis: 83.8 CRLS1 C20orf155, CLS1, dJ967N21.6, GCD10 ENSG00000088766 Cardiolipin synthase 1 20 6006090-6040053 Mitochondrial proteins, Predicted membrane proteins Evidence at transcript level Evidence at transcript level Evidence at transcript level Expressed in all liver: 58.4 CS ENSG00000062485 Citrate synthase 12 56271699-56300392 Citric acid cycle related proteins, Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA038460, HPA038461, CAB075750, CAB075751, CAB075752, CAB075753, CAB075754 Supportive Supportive Mitochondria Expressed in all skeletal muscle: 72.6 CXorf23 ENSG00000173681 Chromosome X open reading frame 23 X 19912860-19970298 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA027215 Uncertain Uncertain Nucleus but not nucleoli Expressed in all endometrium: 4.8 CYB5A CYB5 ENSG00000166347 Cytochrome b5 type A (microsomal) 18 74250847-74292016 Disease related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB006333, HPA047548, HPA058547 Supportive Uncertain Cytoplasm, Vesicles Expressed in all liver: 847.2 CYB5B CYB5-M ENSG00000103018 Cytochrome b5 type B (outer mitochondrial membrane) 16 69424525-69466266 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA007893 Uncertain Uncertain Endoplasmic reticulum, Cytoplasm, Microtubule organizing center Expressed in all adrenal gland: 265.3 CYB5R3 DIA1 ENSG00000100243 Cytochrome b5 reductase 3 22 42617840-42649568 Cancer-related genes, Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA001566 Uncertain Supportive Endoplasmic reticulum Expressed in all adipose tissue: 214.7 CYC1 UQCR4 ENSG00000179091 Cytochrome c-1 8 144095027-144097525 Disease related genes, Mitochondrial proteins, Plasma proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA001247 Supportive Supportive Mitochondria Expressed in all heart muscle: 184.7 CYCS CYC, HCS ENSG00000172115 Cytochrome c, somatic 7 25120091-25125361 Disease related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB004222, CAB005126, CAB018597 Supportive Supportive Mitochondria Expressed in all heart muscle: 215.0 CYP11A1 CYP11A, P450SCC ENSG00000140459 Cytochrome P450, family 11, subfamily A, polypeptide 1 15 74337759-74367740 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA016436 Supportive Tissue enriched 9 adrenal gland: 462.1 placenta: 51.9 CYP11B1 CPN1, CYP11B, FHI, P450C11 ENSG00000160882 Cytochrome P450, family 11, subfamily B, polypeptide 1 8 142872356-142879846 Disease related genes, Enzymes, FDA approved drug targets, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA049171, HPA056348, HPA057752 Supportive Tissue enriched 891 adrenal gland: 1057.2 testis: 1.1 CYP11B2 ALDOS, CPN2, CYP11B, CYP11BL, P-450C18, P450aldo ENSG00000179142 Cytochrome P450, family 11, subfamily B, polypeptide 2 8 142910559-142917843 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA049171, HPA056348, HPA057752 Supportive Tissue enriched 776 adrenal gland: 77.6 adipose tissue: 0.0 CYP24A1 CP24, CYP24, P450-CC24 ENSG00000019186 Cytochrome P450, family 24, subfamily A, polypeptide 1 20 54153449-54173973 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA022261, HPA063771 Supportive Supportive Nucleus but not nucleoli, Mitochondria, Plasma membrane Tissue enhanced 0 endometrium: 11.5;urinary bladder: 40.1 tonsil: 8.0 CYP27A1 CP27, CTX, CYP27 ENSG00000135929 Cytochrome P450, family 27, subfamily A, polypeptide 1 2 218781749-218815293 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA059155 Uncertain Supportive Mitochondria Expressed in all liver: 218.5 CYP27B1 CYP1, P450c1, PDDR, VDD1 ENSG00000111012 Cytochrome P450, family 27, subfamily B, polypeptide 1 12 57762334-57768986 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level HPA043358 Uncertain Nucleus but not nucleoli, Cytoplasm Group enriched 6 kidney: 6.6;thyroid gland: 1.9 lymph node: 0.6 D2HGDH D2HGD, FLJ42195, MGC25181 ENSG00000180902 D-2-hydroxyglutarate dehydrogenase 2 241734579-241768816 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA056216 Uncertain Expressed in all skin: 29.4 DAP3 bMRP-10, DAP-3, DKFZp686G12159, MGC126058, MGC126059, MRP-S29, MRPS29 ENSG00000132676 Death associated protein 3 1 155687960-155739010 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA006076, HPA023687 Supportive Supportive Mitochondria, Nucleus but not nucleoli Expressed in all tonsil: 66.4 DARS2 FLJ10514 ENSG00000117593 Aspartyl-tRNA synthetase 2, mitochondrial 1 173824503-173858546 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA026506, HPA026528 Supportive Supportive Mitochondria, Nucleus Expressed in all rectum: 12.3 DBT ENSG00000137992 Dihydrolipoamide branched chain transacylase E2 1 100186919-100249834 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA026481, HPA026485, HPA026533 Supportive Supportive Mitochondria Expressed in all kidney: 13.0 DDX28 FLJ11282, MDDX28 ENSG00000182810 DEAD (Asp-Glu-Ala-Asp) box polypeptide 28 16 68021274-68023442 Enzymes, Mitochondrial proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041911, HPA053585 Uncertain Supportive Cytoplasm, Mitochondria, Nucleoli Expressed in all bone marrow: 9.4 DECR1 DECR, SDR18C1 ENSG00000104325 2,4-dienoyl CoA reductase 1, mitochondrial 8 90001405-90052092 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA023160, HPA023162, HPA023238 Supportive Supportive Mitochondria, Cytoplasm Expressed in all liver: 186.0 DGUOK dGK ENSG00000114956 Deoxyguanosine kinase 2 73926826-73958961 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA034766, HPA057246 Uncertain Expressed in all fallopian tube: 25.2 DHODH ENSG00000102967 Dihydroorotate dehydrogenase (quinone) 16 72008588-72027664 Disease related genes, Enzymes, FDA approved drug targets, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA010123, HPA011942 Supportive Supportive Nucleus but not nucleoli, Mitochondria Expressed in all liver: 17.6 DHTKD1 DKFZP762M115, KIAA1630, MGC3090 ENSG00000181192 Dehydrogenase E1 and transketolase domain containing 1 10 12068972-12123225 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA037949, HPA037950 Uncertain Supportive Mitochondria Expressed in all liver: 46.9 DHX30 DDX30, FLJ11214, KIAA0890 ENSG00000132153 DEAH (Asp-Glu-Ala-His) box helicase 30 3 47802909-47850195 Enzymes, Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA034805, HPA034806 Supportive Supportive Cytoplasm, Mitochondria Expressed in all testis: 28.9 DHX32 DDX32, DHLP1, FLJ10694, FLJ10889 ENSG00000089876 DEAH (Asp-Glu-Ala-His) box polypeptide 32 10 125836337-125896436 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA048872 Uncertain Expressed in all rectum: 28.3 DIABLO DFNA64, DIABLO-S, FLJ10537, FLJ25049, SMAC ENSG00000184047 Diablo, IAP-binding mitochondrial protein 12 122207662-122227534 Disease related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA001825, CAB003857, CAB016688 Supportive Supportive Mitochondria Expressed in all testis: 55.8 DLAT DLTA, PDC-E2 ENSG00000150768 Dihydrolipoamide S-acetyltransferase 11 112024814-112064390 Citric acid cycle related proteins, Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB003782, HPA040786, HPA062766 Supportive Supportive Mitochondria Expressed in all heart muscle: 25.0 DLD DLDH, GCSL, LAD ENSG00000091140 Dihydrolipoamide dehydrogenase 7 107890970-107931730 Citric acid cycle related proteins, Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA044849 Supportive Supportive Mitochondria Expressed in all heart muscle: 93.3 DLST DLTS ENSG00000119689 Dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex) 14 74881891-74903745 Citric acid cycle related proteins, Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA003010 Supportive Uncertain Nucleus, Cytoplasm, Mitochondria Expressed in all kidney: 56.2 DMGDH ENSG00000132837 Dimethylglycine dehydrogenase 5 78997606-79236038 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA036441, HPA036442 Supportive Group enriched 17 kidney: 107.7;liver: 82.2 adipose tissue: 5.6 DNAJA3 hTid-1, TID1 ENSG00000103423 DnaJ (Hsp40) homolog, subfamily A, member 3 16 4425805-4456775 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB016095, HPA040875, HPA044229 Uncertain Supportive Mitochondria Expressed in all adrenal gland: 28.2 DNAJC19 Pam18, Tim14, TIMM14 ENSG00000205981 DnaJ (Hsp40) homolog, subfamily C, member 19 3 180983709-180989774 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA037782 Uncertain Expressed in all kidney: 17.4 DNM1L DRP1, DVLP, DYMPLE, HDYNIV, VPS1 ENSG00000087470 Dynamin 1-like 12 32679200-32745650 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB009952, HPA039324 Supportive Supportive Cytoplasm, Vesicles Expressed in all cerebral cortex: 45.4 DUT dUTPase ENSG00000128951 Deoxyuridine triphosphatase 15 48331011-48343373 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA054422, HPA060360 Supportive Supportive Nucleus but not nucleoli Expressed in all bone marrow: 83.6 EARS2 KIAA1970, MSE1 ENSG00000103356 Glutamyl-tRNA synthetase 2, mitochondrial 16 23522014-23557731 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA043289, HPA043633 Uncertain Supportive Mitochondria, Nucleus but not nucleoli Expressed in all testis: 9.2 ECH1 HPXEL ENSG00000104823 Enoyl CoA hydratase 1, peroxisomal 19 38815422-38832005 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA002907, HPA005835 Supportive Uncertain Expressed in all skeletal muscle: 266.5 ECHDC2 FLJ10948 ENSG00000121310 Enoyl CoA hydratase domain containing 2 1 52895910-52927212 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA026731, HPA026768 Supportive Expressed in all liver: 59.8 ECHDC3 FLJ20909 ENSG00000134463 Enoyl CoA hydratase domain containing 3 10 11742366-11764070 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA038306 Supportive Uncertain Nucleus, Nucleoli, Mitochondria, Vesicles Expressed in all kidney: 57.7 ECHS1 SCEH ENSG00000127884 Enoyl CoA hydratase, short chain, 1, mitochondrial 10 133362480-133373689 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB003783, HPA021995, HPA022476 Supportive Supportive Mitochondria Expressed in all liver: 351.6 ECI1 DCI ENSG00000167969 Enoyl-CoA delta isomerase 1 16 2239395-2252300 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041746, HPA043227 Supportive Expressed in all kidney: 56.4 ECSIT SITPEC ENSG00000130159 ECSIT signalling integrator 19 11505916-11529174 Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA042979 Uncertain Supportive Nucleus but not nucleoli, Cytoplasm Expressed in all heart muscle: 45.8 ELOVL6 FLJ23378, LCE, MGC5487 ENSG00000170522 ELOVL fatty acid elongase 6 4 110045846-110199199 Enzymes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA042355 Uncertain Mixed rectum: 18.4 ENDOG ENSG00000167136 Endonuclease G 9 128818474-128822677 Mitochondrial proteins, Plasma proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA021335, HPA021830 Uncertain Expressed in all skeletal muscle: 30.9 ENOSF1 HSRTSBETA, rTS, TYMSAS ENSG00000132199 Enolase superfamily member 1 18 670324-712676 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA047829 Supportive Expressed in all kidney: 33.5 ETFA EMA, GA2, MADD ENSG00000140374 Electron-transfer-flavoprotein, alpha polypeptide 15 76215355-76311472 Disease related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA018990, HPA018993, HPA018996, HPA024089 Supportive Supportive Mitochondria Expressed in all liver: 175.4 ETFB ENSG00000105379 Electron-transfer-flavoprotein, beta polypeptide 19 51345169-51366418 Disease related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA018910, HPA018921, HPA018923 Supportive Supportive Mitochondria Expressed in all liver: 145.7 ETFDH ETFQO ENSG00000171503 Electron-transferring-flavoprotein dehydrogenase 4 158672125-158709623 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041978 Supportive Expressed in all liver: 59.0 ETHE1 HSCO, YF13H12 ENSG00000105755 Ethylmalonic encephalopathy 1 19 43506719-43527244 Cancer-related genes, Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA028360, HPA029028, HPA029029 Supportive Supportive Mitochondria, Nucleus but not nucleoli Expressed in all rectum: 173.1 ETNPPL AGXT2L1 ENSG00000164089 Ethanolamine-phosphate phospho-lyase 4 108742040-108763054 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA044546, HPA072938 Uncertain Uncertain Nucleus Group enriched 6 cerebral cortex: 70.2;liver: 69.3;salivary gland: 16.2 stomach: 8.0 EXOG ENDOGL1, ENDOGL2, ENGL, ENGL-a, ENGL-b ENSG00000157036 Endo/exonuclease (5'-3'), endonuclease G-like 3 38496127-38542161 Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA013609 Uncertain Mixed heart muscle: 6.3 FAM65B C6orf32, DIFF48, KIAA0386, MYONAP ENSG00000111913 Family with sequence similarity 65, member B 6 24797373-25042168 Cytoskeleton related proteins, Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA031245 Uncertain Expressed in all lymph node: 68.3 FARS2 dJ236A3.1, FARS1 ENSG00000145982 Phenylalanyl-tRNA synthetase 2, mitochondrial 6 5261044-5771580 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA018148, HPA028836 Uncertain Uncertain Plasma membrane Expressed in all fallopian tube: 20.5 FDX1 ADX, FDX ENSG00000137714 Ferredoxin 1 11 110429883-110464881 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041630, HPA062087 Supportive Supportive Mitochondria Tissue enriched 13 adrenal gland: 251.5 kidney: 18.9 FDX1L MGC19604 ENSG00000267673 Ferredoxin 1-like 19 10310045-10316015 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA043986 Uncertain Expressed in all thyroid gland: 15.5 FDXR ADXR ENSG00000161513 Ferredoxin reductase 17 74862497-74873031 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB009818, HPA044393, HPA053673 Supportive Tissue enhanced 0 adrenal gland: 126.6 testis: 26.5 FECH ENSG00000066926 Ferrochelatase 18 57548283-57586772 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB033205, HPA044100, HPA048177 Supportive Expressed in all bone marrow: 81.7 FH fumarase ENSG00000091483 Fumarate hydratase 1 241497603-241519761 Cancer-related genes, Citric acid cycle related proteins, Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB017785, HPA025770, HPA025948, HPA027341 Supportive Uncertain Supportive Mitochondria Expressed in all heart muscle: 87.2 FIBP FGFIBP ENSG00000172500 Fibroblast growth factor (acidic) intracellular binding protein 11 65883741-65888539 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA011729 Uncertain Supportive Nucleus Expressed in all testis: 43.4 FIS1 CGI-135, Fis1, H_NH0132A01.6, TTC11 ENSG00000214253 Fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae) 7 101239458-101252316 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA017430 Uncertain Supportive Mitochondria Expressed in all fallopian tube: 161.8 FKBP8 FKBP38, FKBPr38 ENSG00000105701 FK506 binding protein 8, 38kDa 19 18531751-18544077 Cancer-related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB025346, HPA045177 Supportive Supportive Mitochondria, Cytoplasm, Endoplasmic reticulum Expressed in all testis: 176.6 FPGS ENSG00000136877 Folylpolyglutamate synthase 9 127794597-127814327 Enzymes, Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA050488 Uncertain Expressed in all ovary: 21.4 FTMT MtF ENSG00000181867 Ferritin mitochondrial 5 121851955-121852833 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA043650 Uncertain Tissue enriched 243 testis: 24.2 adipose tissue: 0.0 FUNDC2 DC44, HCBP6 ENSG00000165775 FUN14 domain containing 2 X 155025980-155060303 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA059129 Uncertain Mixed skeletal muscle: 3.0 FXN CyaY, FA, FARR, FRDA, X25 ENSG00000165060 Frataxin 9 69035259-69100178 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted secreted proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level CAB022164 Uncertain Expressed in all bone marrow: 16.5 GATB PET112, PET112L ENSG00000059691 Glutamyl-tRNA(Gln) amidotransferase, subunit B 4 151670504-151761023 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA042610 Uncertain Supportive Mitochondria Expressed in all heart muscle: 17.1 GATM AGAT ENSG00000171766 Glycine amidinotransferase (L-arginine:glycine amidinotransferase) 15 45361124-45402327 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA026077 Supportive Supportive Mitochondria Group enriched 7 kidney: 1148.8;liver: 723.4;pancreas: 552.8 duodenum: 122.5 GBAS NIPSNAP2 ENSG00000146729 Glioblastoma amplified sequence 7 55951793-56000181 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA063084 Supportive Supportive Mitochondria Expressed in all skeletal muscle: 166.5 GCAT KBL ENSG00000100116 Glycine C-acetyltransferase 22 37807905-37817176 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA020460 Uncertain Supportive Nucleus but not nucleoli, Mitochondria Expressed in all pancreas: 29.2 GCDH ACAD5 ENSG00000105607 Glutaryl-CoA dehydrogenase 19 12891026-12914207 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA043252, HPA048492 Supportive Supportive Mitochondria Expressed in all liver: 37.4 GCSH ENSG00000140905 Glycine cleavage system protein H (aminomethyl carrier) 16 81081961-81096403 Disease related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041368 Uncertain Mixed kidney: 4.8 GFM1 EFGM, EGF1, GFM ENSG00000168827 G elongation factor, mitochondrial 1 3 158644278-158692575 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA034764, HPA034765, HPA061405 Supportive Uncertain Mitochondria, Nucleus Expressed in all kidney: 31.0 GFM2 EFG2, FLJ21661 ENSG00000164347 G elongation factor, mitochondrial 2 5 74721204-74767371 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA036863, HPA036864 Uncertain Supportive Nucleus but not nucleoli Expressed in all fallopian tube: 23.1 GIMAP5 HIMAP3, IAN4L1, IAN5 ENSG00000196329 GTPase, IMAP family member 5 7 150716557-150750033 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA015102 Uncertain Mixed lymph node: 45.8 GIMAP8 DKFZp667I133, hIAN6, IAN9 ENSG00000171115 GTPase, IMAP family member 8 7 150450630-150479392 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA014474, HPA017765 Supportive Supportive Nucleus but not nucleoli, Cytoplasm Mixed spleen: 31.7 GK GK1, GKD ENSG00000198814 Glycerol kinase X 30653359-30731456 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA060687 Uncertain Mixed small intestine: 36.7 GK2 GKP2, GKTA ENSG00000196475 Glycerol kinase 2 4 79406352-79408293 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA060687 Uncertain Tissue enriched 694 testis: 69.3 adipose tissue: 0.0 GLDC GCSP, NKH ENSG00000178445 Glycine dehydrogenase (decarboxylating) 9 6532464-6645650 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA002318, HPA052887 Supportive Supportive Mitochondria, Nucleus Tissue enhanced 0 kidney: 19.2;liver: 11.4;placenta: 12.5 cerebral cortex: 4.5 GLOD4 C17orf25, CGI-150, HC71 ENSG00000167699 Glyoxalase domain containing 4 17 757097-783390 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA021623, HPA023246, HPA023248 Supportive Uncertain Cytoplasm, Nucleus, Nucleoli Expressed in all kidney: 58.7 GLRX2 bA101E13.1, GRX2 ENSG00000023572 Glutaredoxin 2 1 193096468-193106114 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA023087, HPA057224 Supportive Supportive Nucleus but not nucleoli Expressed in all prostate: 24.3 GLS GLS1, KIAA0838 ENSG00000115419 Glutaminase 2 190880827-190965552 Enzymes, Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA036223 Supportive Supportive Mitochondria Expressed in all kidney: 208.3 GLS2 GA, GLS, hLGA, LGA ENSG00000135423 Glutaminase 2 (liver, mitochondrial) 12 56470944-56488414 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA038608 Uncertain Tissue enriched 12 liver: 41.1 cerebral cortex: 3.4 GLUD1 GDH, GLUD ENSG00000148672 Glutamate dehydrogenase 1 10 87050486-87094866 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA042492, HPA044839 Uncertain Supportive Mitochondria Expressed in all liver: 191.7 GLUD2 GLUDP1 ENSG00000182890 Glutamate dehydrogenase 2 X 121047588-121050080 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA042492, HPA044839 Uncertain Supportive Mitochondria Expressed in all liver: 87.4 GLYAT ACGNAT, GAT ENSG00000149124 Glycine-N-acyltransferase 11 58640426-58731974 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Group enriched 7 kidney: 271.3;liver: 165.4 adipose tissue: 31.0 GLYATL1 FLJ34646, MGC15397 ENSG00000166840 Glycine-N-acyltransferase-like 1 11 58905398-59043527 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA039501 Supportive Uncertain Golgi apparatus, Cytoplasm Group enriched 12 kidney: 73.8;liver: 164.2 prostate: 10.1 GLYATL2 BXMAS2-10, MGC24009 ENSG00000156689 Glycine-N-acyltransferase-like 2 11 58834065-58904215 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level HPA060292 Uncertain Group enriched 6 gallbladder: 7.1;salivary gland: 3.4 prostate: 0.8 GLYCTK HBEBP2, HBEBP4 ENSG00000168237 Glycerate kinase 3 52287089-52293476 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA006913 Uncertain Supportive Cytoplasm, Golgi apparatus Tissue enhanced 0 duodenum: 28.2;liver: 36.3 small intestine: 21.4 GOT2 KAT4, KATIV, mitAAT ENSG00000125166 Glutamic-oxaloacetic transaminase 2, mitochondrial 16 58707131-58734357 Cancer-related genes, Candidate cardiovascular disease genes, Enzymes, Mitochondrial proteins, Plasma proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA018139 Supportive Expressed in all skeletal muscle: 189.7 GPAM GPAT1, KIAA1560, MGC26846 ENSG00000119927 Glycerol-3-phosphate acyltransferase, mitochondrial 10 112149864-112215377 Enzymes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA046339 Uncertain Tissue enriched 7 adipose tissue: 215.9 liver: 31.7 GPD2 ENSG00000115159 Glycerol-3-phosphate dehydrogenase 2 (mitochondrial) 2 156435290-156613735 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA008012, HPA045506 Supportive Expressed in all fallopian tube: 21.1 GPX1 ENSG00000233276 Glutathione peroxidase 1 3 49357176-49358600 Cancer-related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB011582, HPA044758 Supportive Supportive Cytoplasm Expressed in all adipose tissue: 174.3 GPX4 MCSP, PHGPx ENSG00000167468 Glutathione peroxidase 4 19 1103926-1106791 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB008630, HPA058546 Uncertain Supportive Nucleus but not nucleoli, Mitochondria Expressed in all testis: 652.9 GRAMD4 DIP, KIAA0767 ENSG00000075240 GRAM domain containing 4 22 46576012-46679790 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA029502 Uncertain Expressed in all skin: 30.8 GRPEL1 FLJ25609, HMGE ENSG00000109519 GrpE-like 1, mitochondrial (E. coli) 4 7058906-7068197 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA036647 Supportive Supportive Mitochondria, Nucleus Expressed in all adrenal gland: 28.6 GRPEL2 DKFZp451C205, FLJ23713, Mt-GrpE#2 ENSG00000164284 GrpE-like 2, mitochondrial (E. coli) 5 149345430-149354583 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA018173, HPA023211 Supportive Supportive Mitochondria Expressed in all esophagus: 23.9 GSR ENSG00000104687 Glutathione reductase 8 30678061-30727926 Cancer-related genes, Enzymes, FDA approved drug targets, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA001538, CAB008632 Supportive Supportive Cytoplasm, Plasma membrane Expressed in all rectum: 46.8 GTPBP3 FLJ14700, GTPBG3, MSS1, MTGP1, THDF1 ENSG00000130299 GTP binding protein 3 (mitochondrial) 19 17334920-17342735 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA042158 Uncertain Supportive Mitochondria Expressed in all skin: 7.4 HADH HADH1, HADHSC, SCHAD ENSG00000138796 Hydroxyacyl-CoA dehydrogenase 4 107989714-108035175 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA039588, HPA043888 Supportive Supportive Mitochondria, Nucleus but not nucleoli Expressed in all kidney: 108.2 HADHA GBP, LCEH, LCHAD, MTPA ENSG00000084754 Hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit 2 26190635-26244726 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA015536, HPA056070 Uncertain Supportive Mitochondria Expressed in all duodenum: 151.4 HADHB MTPB ENSG00000138029 Hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit 2 26243170-26290468 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA037539, HPA037540, HPA066099 Supportive Supportive Mitochondria Expressed in all heart muscle: 249.3 HARS2 HARSL, HARSR, HO3 ENSG00000112855 Histidyl-tRNA synthetase 2, mitochondrial 5 140691426-140699291 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted secreted proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA035941 Uncertain Uncertain Cytoplasm Expressed in all rectum: 19.0 HAX1 HCLSBP1, HS1BP1 ENSG00000143575 HCLS1 associated protein X-1 1 154272511-154275875 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA055141 Uncertain Expressed in all heart muscle: 77.9 HCCS CCHL, MLS ENSG00000004961 Holocytochrome c synthase X 11111301-11123078 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA002946 Uncertain Supportive Mitochondria Expressed in all heart muscle: 25.9 HCLS1 CTTNL, HS1 ENSG00000180353 Hematopoietic cell-specific Lyn substrate 1 3 121631399-121660927 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA019143 Supportive Expressed in all tonsil: 201.0 HIBADH NS5ATP1 ENSG00000106049 3-hydroxyisobutyrate dehydrogenase 7 27525442-27662995 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA019522, HPA021002 Supportive Expressed in all kidney: 58.4 HIBCH ENSG00000198130 3-hydroxyisobutyryl-CoA hydrolase 2 190189735-190344193 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA036540, HPA036541 Supportive Uncertain Nucleus but not nucleoli, Mitochondria Expressed in all kidney: 124.2 HINT2 ENSG00000137133 Histidine triad nucleotide binding protein 2 9 35812960-35815354 Mitochondrial proteins, Plasma proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA020961, HPA059109 Uncertain Supportive Mitochondria Expressed in all kidney: 57.1 HK1 ENSG00000156515 Hexokinase 1 10 69269984-69401882 Cancer-related genes, Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA007043, HPA007044, CAB010052, HPA011956 Supportive Supportive Mitochondria Expressed in all testis: 87.6 HK2 ENSG00000159399 Hexokinase 2 2 74833981-74893359 Cancer-related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA028587 Uncertain Expressed in all adipose tissue: 36.8 HLCS HCS ENSG00000159267 Holocarboxylase synthetase (biotin-(proprionyl-CoA-carboxylase (ATP-hydrolysing)) ligase) 21 36750888-36990236 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA017379 Uncertain Supportive Cytoplasm Expressed in all thyroid gland: 12.2 HMGCL HL ENSG00000117305 3-hydroxymethyl-3-methylglutaryl-CoA lyase 1 23801885-23838620 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA004727 Supportive Expressed in all liver: 92.8 HMGCS2 ENSG00000134240 3-hydroxy-3-methylglutaryl-CoA synthase 2 (mitochondrial) 1 119747996-119768905 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA027423, HPA027442, CAB032906 Supportive Supportive Mitochondria Tissue enhanced 0 colon: 278.4;liver: 755.2 rectum: 188.9 HOGA1 C10orf65, DHDPS2, DHDPSL, FLJ37472, NPL2 ENSG00000241935 4-hydroxy-2-oxoglutarate aldolase 1 10 97584323-97612802 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA039466 Uncertain Tissue enhanced 0 kidney: 45.0;liver: 16.3 heart muscle: 7.6 HSCB DNAJC20, HSC20, Jac1 ENSG00000100209 HscB mitochondrial iron-sulfur cluster co-chaperone 22 28742031-28757515 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA018447, HPA031518 Uncertain Supportive Nucleus, Cytoplasm, Mitochondria Expressed in all urinary bladder: 8.8 HSD17B10 17b-HSD10, ABAD, CAMR, ERAB, HADH2, MHBD, MRPP2, MRXS10, SDR5C1 ENSG00000072506 Hydroxysteroid (17-beta) dehydrogenase 10 X 53431258-53434373 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA001432 Uncertain Uncertain Nucleus, Nuclear membrane, Golgi apparatus Expressed in all liver: 95.3 HSD3B1 HSD3B, HSDB3, SDR11E1 ENSG00000203857 Hydroxy-delta-5-steroid dehydrogenase, 3 beta- and steroid delta-isomerase 1 1 119507198-119515054 Enzymes, FDA approved drug targets, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA043261, HPA043264, HPA044028 Supportive Tissue enriched 17 placenta: 90.5 small intestine: 5.4 HSD3B2 SDR11E2 ENSG00000203859 Hydroxy-delta-5-steroid dehydrogenase, 3 beta- and steroid delta-isomerase 2 1 119414931-119423035 Disease related genes, Enzymes, FDA approved drug targets, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA043261, HPA043264, HPA044028 Supportive Tissue enriched 557 adrenal gland: 1546.1 testis: 2.7 HSPA1A HSP70-1, HSPA1 ENSG00000204389 Heat shock 70kDa protein 1A 6 31815464-31817946 Cancer-related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level CAB017451, CAB032815, HPA052504 Supportive Supportive Nucleus but not nucleoli, Cytoplasm Expressed in all adrenal gland: 369.9 HSPA1B HSP70-2 ENSG00000204388 Heat shock 70kDa protein 1B 6 31827735-31830255 Cancer-related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level CAB008640, HPA052504 Uncertain Supportive Cytoplasm Expressed in all adrenal gland: 357.8 HSPA9 GRP75, HSPA9B, mot-2, mthsp75, PBP74 ENSG00000113013 Heat shock 70kDa protein 9 (mortalin) 5 138554882-138575444 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA000898, CAB005219 Supportive Supportive Mitochondria Expressed in all adrenal gland: 141.3 HSPD1 GROEL, HSP60, SPG13 ENSG00000144381 Heat shock 60kDa protein 1 (chaperonin) 2 197486581-197516737 Cancer-related genes, Disease related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA001523, CAB002775, HPA050025, CAB072816 Supportive Supportive Mitochondria Expressed in all adrenal gland: 331.2 HSPE1 CPN10, GROES ENSG00000115541 Heat shock 10kDa protein 1 2 197499994-197503457 Cancer-related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB017366, HPA038755, HPA048272 Supportive Expressed in all adrenal gland: 233.3 HTRA2 OMI, PARK13, PRSS25 ENSG00000115317 HtrA serine peptidase 2 2 74529377-74533348 Cytoskeleton related proteins, Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB004004, HPA027366 Uncertain Expressed in all spleen: 6.6 IARS2 FLJ10326 ENSG00000067704 Isoleucyl-tRNA synthetase 2, mitochondrial 1 220094102-220148041 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA024212, HPA024594, HPA024596 Supportive Supportive Mitochondria Expressed in all rectum: 46.3 IBA57 C1orf69, FLJ12734 ENSG00000181873 IBA57, iron-sulfur cluster assembly homolog (S. cerevisiae) 1 228165815-228182257 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA030555, HPA030557 Uncertain Expressed in all bone marrow: 2.1 IDH2 ENSG00000182054 Isocitrate dehydrogenase 2 (NADP+), mitochondrial 15 90083045-90102504 Cancer-related genes, Citric acid cycle related proteins, Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA007831 Supportive Supportive Mitochondria Expressed in all skeletal muscle: 346.7 IDH3A ENSG00000166411 Isocitrate dehydrogenase 3 (NAD+) alpha 15 78131498-78171949 Citric acid cycle related proteins, Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041465, HPA062971 Supportive Supportive Mitochondria Expressed in all heart muscle: 33.6 IDH3B RP46 ENSG00000101365 Isocitrate dehydrogenase 3 (NAD+) beta 20 2658395-2664219 Citric acid cycle related proteins, Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA049387, HPA054180 Supportive Supportive Mitochondria Expressed in all heart muscle: 72.4 IDH3G ENSG00000067829 Isocitrate dehydrogenase 3 (NAD+) gamma X 153785766-153794523 Citric acid cycle related proteins, Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA000425, HPA002017 Supportive Supportive Mitochondria Expressed in all fallopian tube: 43.3 IMMP1L FLJ25059 ENSG00000148950 IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae) 11 31432401-31509645 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA038372 Uncertain Expressed in all heart muscle: 12.5 IMMP2L IMMP2L-IT1, IMP2 ENSG00000184903 IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae) 7 110663051-111562517 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA026711 Uncertain Uncertain Mitochondria Expressed in all smooth muscle: 48.1 IMMT HMP, MINOS2, P87, P89 ENSG00000132305 Inner membrane protein, mitochondrial 2 86143932-86195770 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB022439, HPA036164, HPA036165 Supportive Supportive Mitochondria Expressed in all heart muscle: 82.9 ISCA1 HBLD2, hIscA, ISA1, MGC4276 ENSG00000135070 Iron-sulfur cluster assembly 1 9 86264546-86282538 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA042789 Uncertain Expressed in all adrenal gland: 34.4 ISCA2 HBLD1, ISA2 ENSG00000165898 Iron-sulfur cluster assembly 2 14 74493720-74497106 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA030492 Uncertain Expressed in all fallopian tube: 20.3 ISCU hnifU, IscU, ISU2, NIFUN ENSG00000136003 Iron-sulfur cluster assembly enzyme 12 108562582-108569384 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB006329, HPA038602, HPA057592 Uncertain Supportive Cytoplasm Expressed in all adrenal gland: 258.4 IVD ACAD2 ENSG00000128928 Isovaleryl-CoA dehydrogenase 15 40405795-40435947 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041391, HPA044250 Supportive Supportive Mitochondria, Nucleus but not nucleoli Expressed in all thyroid gland: 90.0 KIAA0101 NS5ATP9, OEATC-1, p15(PAF), PAF15 ENSG00000166803 KIAA0101 15 64364311-64387687 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA055444 Supportive Nucleus, Cytoplasm Tissue enhanced 0 bone marrow: 78.2 lymph node: 46.7 KIAA1279 DKFZP586B0923, TTC20 ENSG00000198954 KIAA1279 10 68988731-69016982 Cytoskeleton related proteins, Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA035538, HPA035539 Uncertain Expressed in all cerebral cortex: 26.9 KIF1B CMT2, CMT2A, HMSNII, KIAA0591, KLP ENSG00000054523 Kinesin family member 1B 1 10210805-10381603 Disease related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB015177, HPA026434 Uncertain Uncertain Nucleoli, Cytoplasm Expressed in all cerebral cortex: 54.0 KLK6 Bssp, Klk7, neurosin, PRSS18, PRSS9 ENSG00000167755 Kallikrein-related peptidase 6 19 50958631-50969673 Cancer-related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA051837 Supportive Nucleus but not nucleoli, Cytoskeleton (Microtubules) Tissue enhanced 0 cerebral cortex: 36.6;esophagus: 48.8;fallopian tube: 29.4;tonsil: 29.6 kidney: 8.2 KMO ENSG00000117009 Kynurenine 3-monooxygenase (kynurenine 3-hydroxylase) 1 241532134-241595642 Enzymes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA031115 Uncertain Tissue enhanced 0 kidney: 17.2;liver: 21.1 tonsil: 7.8 L2HGDH C14orf160, FLJ12618 ENSG00000087299 L-2-hydroxyglutarate dehydrogenase 14 50237563-50312548 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA065409, HPA069708 Uncertain Supportive Mitochondria Expressed in all kidney: 13.3 LACTB FLJ14902, MRPL56 ENSG00000103642 Lactamase, beta 15 63121800-63142061 Enzymes, Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA036361, HPA036362 Supportive Supportive Mitochondria, Cytoplasm Expressed in all bone marrow: 23.0 LARS2 KIAA0028, LEURS, MGC26121 ENSG00000011376 Leucyl-tRNA synthetase 2, mitochondrial 3 45388506-45549421 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA035951, HPA045450, HPA066085 Uncertain Supportive Nucleus but not nucleoli, Mitochondria Expressed in all kidney: 9.1 LDHD ENSG00000166816 Lactate dehydrogenase D 16 75111860-75116771 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041766, HPA048639, HPA066148 Uncertain Uncertain Cytoplasm Mixed kidney: 34.1 LETM1 ENSG00000168924 Leucine zipper-EF-hand containing transmembrane protein 1 4 1811479-1856247 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA011029, HPA011100 Supportive Supportive Mitochondria Expressed in all colon: 16.1 LETM2 FLJ25409 ENSG00000165046 Leucine zipper-EF-hand containing transmembrane protein 2 8 38386207-38409527 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA025032, HPA053676 Uncertain Uncertain Nucleus, Cytoplasm Tissue enriched 9 testis: 15.7 stomach: 1.7 LIAS LAS ENSG00000121897 Lipoic acid synthetase 4 39459000-39477653 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA018842, HPA019076 Supportive Uncertain Uncertain Nucleus but not nucleoli, Mitochondria Expressed in all testis: 14.3 LIPT1 MGC12290, MGC13378 ENSG00000144182 Lipoyltransferase 1 2 99154955-99163157 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA034802 Uncertain Expressed in all testis: 11.7 LONP1 hLON, LonHS, PIM1, PRSS15 ENSG00000196365 Lon peptidase 1, mitochondrial 19 5691834-5720572 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA002034, HPA002192 Supportive Supportive Mitochondria, Nucleus Expressed in all adrenal gland: 82.0 LRPPRC GP130, LRP130, LSFC ENSG00000138095 Leucine-rich pentatricopeptide repeat containing 2 43886508-43996005 Cytoskeleton related proteins, Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB033786, HPA036408, HPA036409 Supportive Supportive Mitochondria Expressed in all colon: 41.3 LRRK2 DKFZp434H2111, FLJ45829, PARK8, RIPK7, ROCO2 ENSG00000188906 Leucine-rich repeat kinase 2 12 40196744-40369285 Cancer-related genes, Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA014293, CAB037160 Uncertain Tissue enhanced 0 lung: 36.1 appendix: 9.0 MAATS1 AAT1, AAT1alpha, C3orf15, CaM-IP2, SPATA26 ENSG00000183833 MYCBP-associated, testis expressed 1 3 119703022-119767102 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Tissue enhanced 0 fallopian tube: 14.7 testis: 7.4 MAOA ENSG00000189221 Monoamine oxidase A X 43654907-43746824 Disease related genes, Enzymes, FDA approved drug targets, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB009437, HPA054807, HPA059299 Supportive Supportive Mitochondria Mixed small intestine: 178.7 MAOB ENSG00000069535 Monoamine oxidase B X 43766611-43882447 Enzymes, FDA approved drug targets, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA002328, CAB037200 Supportive Uncertain Nucleoli, Mitochondria Mixed ovary: 130.8 MAP1S BPY2IP1, C19orf5, FLJ10669, MAP8, VCY2IP1 ENSG00000130479 Microtubule-associated protein 1S 19 17719242-17734516 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA050934, HPA054637 Uncertain Supportive Cytoplasm Expressed in all testis: 14.0 MAPK12 ERK6, p38gamma, PRKM12, SAPK-3, SAPK3 ENSG00000188130 Mitogen-activated protein kinase 12 22 50245450-50261825 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB025483, HPA054562 Uncertain Supportive Nucleus but not nucleoli, Cytoplasm Tissue enriched 10 skeletal muscle: 66.1 prostate: 6.6 MARC1 FLJ22390, MOSC1 ENSG00000186205 Mitochondrial amidoxime reducing component 1 1 220786759-220819657 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA028702 Uncertain Uncertain Mitochondria, Nucleus Expressed in all adipose tissue: 149.9 MARC2 FLJ20605, MOSC2 ENSG00000117791 Mitochondrial amidoxime reducing component 2 1 220748225-220784815 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA015085, HPA017572 Supportive Uncertain Nucleus but not nucleoli, Cytoplasm Mixed kidney: 79.0 MARCH5 FLJ20445, MARCH-V, RNF153 ENSG00000198060 Membrane-associated ring finger (C3HC4) 5 10 92291163-92353964 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA052901, HPA056596 Uncertain Supportive Mitochondria Expressed in all thyroid gland: 15.9 MARS2 mtMetRS, SPAX3 ENSG00000247626 Methionyl-tRNA synthetase 2, mitochondrial 2 197705369-197708387 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA035589, HPA035590 Uncertain Uncertain Cytoplasm, Cytoskeleton (Intermediate filaments) Expressed in all tonsil: 5.7 MCAT fabD, FASN2C, MCT, MT, NET62 ENSG00000100294 Malonyl CoA:ACP acyltransferase (mitochondrial) 22 43132206-43143394 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA035471 Uncertain Expressed in all kidney: 16.3 MCCC1 MCCA ENSG00000078070 Methylcrotonoyl-CoA carboxylase 1 (alpha) 3 183015218-183116075 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA008310 Uncertain Supportive Mitochondria Expressed in all kidney: 37.3 MCCC2 MCCB ENSG00000131844 Methylcrotonoyl-CoA carboxylase 2 (beta) 5 71587288-71658704 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA038300, HPA038301, HPA061546 Supportive Supportive Mitochondria Expressed in all prostate: 46.1 MCCD1 ENSG00000204511 Mitochondrial coiled-coil domain 1 6 31528717-31530232 Mitochondrial proteins, Predicted secreted proteins Evidence at transcript level Evidence at transcript level Evidence at transcript level HPA046948 Uncertain Tissue enriched 251 kidney: 25.1 adipose tissue: 0.0 MCEE GLOD2 ENSG00000124370 Methylmalonyl CoA epimerase 2 71109684-71130239 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA035196 Uncertain Uncertain Nucleoli Expressed in all liver: 23.2 MCL1 BCL2L3, Mcl-1 ENSG00000143384 Myeloid cell leukemia 1 1 150574551-150579738 Cancer-related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB002781, HPA008455, HPA031125, CAB068195 Uncertain Supportive Nucleus, Mitochondria Expressed in all bone marrow: 471.7 MCUR1 C6orf79, CCDC90A, FLJ20958 ENSG00000050393 Mitochondrial calcium uniporter regulator 1 6 13786557-13814568 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA055189 Uncertain Expressed in all kidney: 17.2 MDH2 ENSG00000146701 Malate dehydrogenase 2, NAD (mitochondrial) 7 76048051-76067508 Citric acid cycle related proteins, Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA019714, HPA019716, HPA019848, HPA026720 Supportive Supportive Mitochondria Expressed in all skeletal muscle: 186.7 ME2 ENSG00000082212 Malic enzyme 2, NAD(+)-dependent, mitochondrial 18 50879049-50954257 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA008247, HPA008880 Supportive Supportive Mitochondria, Vesicles Expressed in all duodenum: 36.3 ME3 ENSG00000151376 Malic enzyme 3, NADP(+)-dependent, mitochondrial 11 86441108-86672636 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA038473 Uncertain Expressed in all ovary: 14.1 MECR CGI-63, FASN2B, NRBF1 ENSG00000116353 Mitochondrial trans-2-enoyl-CoA reductase 1 29192873-29230942 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA022018, HPA022030, HPA028740 Supportive Supportive Mitochondria Expressed in all skeletal muscle: 11.7 METTL17 FLJ20859, METT11D1 ENSG00000165792 Methyltransferase like 17 14 20989770-20997035 Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA002955, HPA059802 Uncertain Supportive Nucleus Expressed in all rectum: 19.2 MFF C2orf33, GL004 ENSG00000168958 Mitochondrial fission factor 2 227325151-227357836 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA010968 Uncertain Expressed in all testis: 161.4 MFN1 FLJ20693 ENSG00000171109 Mitofusin 1 3 179347692-179394931 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB033437, HPA059230 Uncertain Supportive Mitochondria Expressed in all heart muscle: 11.4 MFN2 CMT2A2, CPRP1, KIAA0214, MARF ENSG00000116688 Mitofusin 2 1 11980181-12013514 Disease related genes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA030554 Uncertain Expressed in all heart muscle: 168.7 MGST1 GST12, MGST-I ENSG00000008394 Microsomal glutathione S-transferase 1 12 16347142-16609259 Enzymes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA044840 Supportive Uncertain Mitochondria, Endoplasmic reticulum Expressed in all liver: 995.7 MIPEP MIP ENSG00000027001 Mitochondrial intermediate peptidase 13 23730189-23889419 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA030676, HPA031669, HPA031670 Uncertain Supportive Mitochondria Expressed in all heart muscle: 38.6 MLXIP bHLHe36, KIAA0867, MIR, MONDOA ENSG00000175727 MLX interacting protein 12 122078722-122147347 Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins, Transcription factors Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA023084 Uncertain Expressed in all colon: 35.7 MLYCD hMCD, MCD ENSG00000103150 Malonyl-CoA decarboxylase 16 83899126-83927026 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA031625 Uncertain Mixed heart muscle: 2.7 MMAB cblB, CFAP23 ENSG00000139428 Methylmalonic aciduria (cobalamin deficiency) cblB type 12 109553737-109573874 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA039017 Uncertain Uncertain Mitochondria Expressed in all adrenal gland: 20.2 MMADHC C2orf25, cblD, CL25022 ENSG00000168288 Methylmalonic aciduria (cobalamin deficiency) cblD type, with homocystinuria 2 149569634-149587816 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA037531, HPA037532 Supportive Expressed in all tonsil: 75.3 MPC1 BRP44L, CGI-129, dJ68L15.3 ENSG00000060762 Mitochondrial pyruvate carrier 1 6 166364919-166383013 Disease related genes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA045119, HPA055790 Supportive Supportive Mitochondria Expressed in all heart muscle: 356.5 MPST MST, TST2 ENSG00000128309 Mercaptopyruvate sulfurtransferase 22 37019635-37029822 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA001240 Uncertain Uncertain Mitochondria, Cytoplasm Expressed in all duodenum: 74.6 MPV17 SYM1 ENSG00000115204 MpV17 mitochondrial inner membrane protein 2 27309492-27325680 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Expressed in all adrenal gland: 47.6 MRM1 FLJ22578 ENSG00000278619 Mitochondrial rRNA methyltransferase 1 homolog (S. cerevisiae) 17 36601572-36608971 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level HPA021598 Supportive Supportive Mitochondria Expressed in all spleen: 3.6 MRPL1 BM022 ENSG00000169288 Mitochondrial ribosomal protein L1 4 77862520-77952790 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA043656 Supportive Supportive Mitochondria Expressed in all rectum: 23.7 MRPL10 L10MT, MGC17973, MRP-L10, MRP-L8, MRPL8, RPML8 ENSG00000159111 Mitochondrial ribosomal protein L10 17 47823272-47831534 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA021234, HPA029885 Supportive Supportive Mitochondria Expressed in all ovary: 40.9 MRPL11 ENSG00000174547 Mitochondrial ribosomal protein L11 11 66435075-66466738 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA057685 Uncertain Expressed in all colon: 15.0 MRPL12 MRPL7, MRPL7/L12, RPML12 ENSG00000262814 Mitochondrial ribosomal protein L12 17 81703357-81707526 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA022853, HPA023043 Supportive Supportive Mitochondria Expressed in all skeletal muscle: 44.8 MRPL13 L13, L13A, L13mt, RPL13, RPML13 ENSG00000172172 Mitochondrial ribosomal protein L13 8 120380761-120445402 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA060899 Uncertain Expressed in all rectum: 36.3 MRPL14 MRP-L32, RPML32 ENSG00000180992 Mitochondrial ribosomal protein L14 6 44113454-44127457 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA038769 Uncertain Expressed in all lung: 48.3 MRPL15 HSPC145, L15mt, MRP-L15, MRP-L7, RPML7 ENSG00000137547 Mitochondrial ribosomal protein L15 8 54135210-54147901 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA044425 Supportive Expressed in all heart muscle: 63.3 MRPL16 FLJ20484, PNAS-111 ENSG00000166902 Mitochondrial ribosomal protein L16 11 59806135-59810872 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA054133 Supportive Expressed in all heart muscle: 35.5 MRPL17 MRP-L26, RPML26 ENSG00000158042 Mitochondrial ribosomal protein L17 11 6680782-6683401 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA043666, HPA050552 Uncertain Uncertain Nucleoli, Golgi apparatus, Vesicles Expressed in all esophagus: 32.5 MRPL18 HSPC071 ENSG00000112110 Mitochondrial ribosomal protein L18 6 159789812-159798436 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA028774, HPA028775 Uncertain Expressed in all fallopian tube: 49.3 MRPL19 KIAA0104, MRP-L15, RLX1, RPML15 ENSG00000115364 Mitochondrial ribosomal protein L19 2 75646783-75690851 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA056622 Uncertain Expressed in all kidney: 30.6 MRPL2 CGI-22, MRP-L14, RPML14 ENSG00000112651 Mitochondrial ribosomal protein L2 6 43054029-43059806 Mitochondrial proteins, Predicted secreted proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA007455, HPA064814 Uncertain Supportive Mitochondria, Nucleus, Cytoplasm Expressed in all heart muscle: 15.3 MRPL20 FLJ10024 ENSG00000242485 Mitochondrial ribosomal protein L20 1 1401908-1407313 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA047074 Supportive Supportive Mitochondria Expressed in all prostate: 91.6 MRPL21 ENSG00000197345 Mitochondrial ribosomal protein L21 11 68891276-68903835 Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA051657 Uncertain Supportive Mitochondria, Nucleus but not nucleoli Expressed in all heart muscle: 56.6 MRPL22 HSPC158, MRP-L25, RPML25 ENSG00000082515 Mitochondrial ribosomal protein L22 5 154941070-154969411 Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA047063 Uncertain Uncertain Mitochondria Expressed in all urinary bladder: 38.7 MRPL23 L23MRP, RPL23L ENSG00000214026 Mitochondrial ribosomal protein L23 11 1947278-1984522 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA050406 Uncertain Supportive Mitochondria, Nucleoli Expressed in all fallopian tube: 39.1 MRPL24 MRP-L18 ENSG00000143314 Mitochondrial ribosomal protein L24 1 156737303-156741590 Mitochondrial proteins, Predicted secreted proteins, Ribosomal proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA030295 Uncertain Expressed in all fallopian tube: 72.1 MRPL27 ENSG00000108826 Mitochondrial ribosomal protein L27 17 50367857-50373214 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted secreted proteins, Ribosomal proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA021416 Uncertain Expressed in all rectum: 68.4 MRPL28 MAAT1, p15 ENSG00000086504 Mitochondrial ribosomal protein L28 16 367384-370527 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA030594, CAB033542, HPA055589 Supportive Supportive Mitochondria Expressed in all testis: 45.2 MRPL3 MRL3, RPML3 ENSG00000114686 Mitochondrial ribosomal protein L3 3 131462212-131502983 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA043665, HPA060132 Uncertain Uncertain Nucleoli, Cytoplasm Expressed in all fallopian tube: 47.2 MRPL30 MRP-L28, RPML28 ENSG00000185414 Mitochondrial ribosomal protein L30 2 99181079-99197626 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA047255 Uncertain Expressed in all esophagus: 17.4 MRPL32 bMRP-59b, HSPC283, L32mt, MRP-L32 ENSG00000106591 Mitochondrial ribosomal protein L32 7 42932200-42948958 Mitochondrial proteins, Predicted secreted proteins, Ribosomal proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA048965 Uncertain Expressed in all adrenal gland: 48.1 MRPL33 C2orf1, RPL33L ENSG00000243147 Mitochondrial ribosomal protein L33 2 27771717-27988087 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA066872 Uncertain Expressed in all adrenal gland: 339.2 MRPL34 L34mt, MGC24974, MGC2633 ENSG00000130312 Mitochondrial ribosomal protein L34 19 17292609-17306843 Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA049276 Uncertain Uncertain Nucleus, Vesicles, Cytoskeleton (Actin filaments) Expressed in all kidney: 60.2 MRPL35 ENSG00000132313 Mitochondrial ribosomal protein L35 2 86199355-86213794 Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA043482 Uncertain Expressed in all rectum: 53.1 MRPL36 BRIP1, L36mt, MRP-L36, PRPL36, RPMJ ENSG00000171421 Mitochondrial ribosomal protein L36 5 1798386-1801366 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA047238 Uncertain Expressed in all testis: 52.0 MRPL37 MRP-L2, RPML2 ENSG00000116221 Mitochondrial ribosomal protein L37 1 54184041-54225464 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA025767, HPA025826, HPA025951 Supportive Supportive Mitochondria Expressed in all rectum: 43.9 MRPL38 HSPC262, MGC4810, MRP-L3, RPML3 ENSG00000204316 Mitochondrial ribosomal protein L38 17 75898643-75905413 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA023054, HPA023135 Uncertain Supportive Mitochondria Expressed in all fallopian tube: 20.6 MRPL39 C21orf92, FLJ20451, L39mt, MGC104174, MGC3400, MRP-L5, MSTP003, PRED22, PRED66, RPML5 ENSG00000154719 Mitochondrial ribosomal protein L39 21 25585656-25607517 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA018331 Uncertain Expressed in all testis: 42.9 MRPL4 CGI-28 ENSG00000105364 Mitochondrial ribosomal protein L4 19 10251901-10260045 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA051261 Uncertain Uncertain Nucleoli, Nucleus, Cytoplasm Expressed in all lymph node: 21.3 MRPL40 MRP-L22, NLVCF ENSG00000185608 Mitochondrial ribosomal protein L40 22 19431902-19436075 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA006181 Uncertain Supportive Mitochondria, Nucleoli Expressed in all thyroid gland: 20.1 MRPL41 BMRP, MRP-L27, MRPL27, PIG3, RPML27 ENSG00000182154 Mitochondrial ribosomal protein L41 9 137551199-137552555 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA024550, HPA027160 Supportive Supportive Mitochondria Expressed in all skeletal muscle: 41.0 MRPL42 HSPC204, MRP-L31, MRPL31, MRPS32, PTD007, RPML31 ENSG00000198015 Mitochondrial ribosomal protein L42 12 93467488-93516213 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA039398 Uncertain Supportive Mitochondria, Plasma membrane Expressed in all rectum: 34.2 MRPL43 bMRP36a ENSG00000055950 Mitochondrial ribosomal protein L43 10 100969458-100987515 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA073022 Uncertain Nucleus but not nucleoli, Mitochondria Expressed in all thyroid gland: 38.5 MRPL44 FLJ12701, FLJ13990 ENSG00000135900 Mitochondrial ribosomal protein L44 2 223957404-223967714 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA038147, HPA038148 Uncertain Supportive Mitochondria, Nucleus, Plasma membrane Expressed in all lymph node: 26.2 MRPL46 C15orf4, LIECG2, P2ECSL ENSG00000259494 Mitochondrial ribosomal protein L46 15 88459476-88467419 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA050166 Uncertain Supportive Mitochondria, Nucleus but not nucleoli Expressed in all heart muscle: 39.1 MRPL47 CGI-204, NCM1 ENSG00000136522 Mitochondrial ribosomal protein L47 3 179588285-179604654 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA037553, HPA047779 Uncertain Supportive Mitochondria Expressed in all testis: 36.7 MRPL48 CGI-118 ENSG00000175581 Mitochondrial ribosomal protein L48 11 73787316-73865133 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA040241, HPA040864 Supportive Expressed in all fallopian tube: 23.8 MRPL49 C11orf4, L49mt, NOF, NOF1 ENSG00000149792 Mitochondrial ribosomal protein L49 11 65122183-65127371 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA046778 Uncertain Expressed in all adrenal gland: 54.5 MRPL50 FLJ20493, MRP-L50 ENSG00000136897 Mitochondrial ribosomal protein L50 9 101387633-101398614 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA022925, HPA056854 Uncertain Supportive Cytoplasm, Vesicles Expressed in all adrenal gland: 14.0 MRPL51 bMRP64, CDA09, HSPC241, MRP64 ENSG00000111639 Mitochondrial ribosomal protein L51 12 6491886-6493841 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA039923 Uncertain Supportive Mitochondria Expressed in all testis: 113.7 MRPL52 ENSG00000172590 Mitochondrial ribosomal protein L52 14 22829879-22835037 Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA012319 Uncertain Uncertain Mitochondria Expressed in all duodenum: 48.5 MRPL53 ENSG00000204822 Mitochondrial ribosomal protein L53 2 74471958-74473322 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA056185 Uncertain Uncertain Nucleoli Expressed in all heart muscle: 20.5 MRPL54 ENSG00000183617 Mitochondrial ribosomal protein L54 19 3762664-3768575 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA042117, HPA046767 Uncertain Uncertain Mitochondria Expressed in all fallopian tube: 54.5 MRPL55 ENSG00000162910 Mitochondrial ribosomal protein L55 1 228106679-228109312 Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA027641 Uncertain Uncertain Golgi apparatus, Vesicles Expressed in all bone marrow: 27.3 MRPL57 MRP63 ENSG00000173141 Mitochondrial ribosomal protein L57 13 21176645-21179084 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA039779, HPA059370 Supportive Supportive Mitochondria Expressed in all adrenal gland: 13.3 MRPL9 ENSG00000143436 Mitochondrial ribosomal protein L9 1 151759643-151763564 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA008579 Uncertain Supportive Mitochondria Expressed in all lymph node: 33.3 MRPS10 FLJ10567 ENSG00000048544 Mitochondrial ribosomal protein S10 6 42206801-42217865 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA029133, HPA029134 Supportive Uncertain Mitochondria, Cytoskeleton (Actin filaments) Expressed in all esophagus: 30.5 MRPS11 FLJ22512, FLJ23406, HCC-2 ENSG00000181991 Mitochondrial ribosomal protein S11 15 88467453-88480773 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA043752, HPA050345 Supportive Supportive Mitochondria Expressed in all thyroid gland: 10.1 MRPS12 RPMS12, RPS12, RPSM12 ENSG00000128626 Mitochondrial ribosomal protein S12 19 38930548-38933162 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA046775, HPA050633 Uncertain Expressed in all duodenum: 17.3 MRPS14 HSMRPS14 ENSG00000120333 Mitochondrial ribosomal protein S14 1 175010789-175023425 Mitochondrial proteins, Predicted secreted proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA051087 Uncertain Supportive Nuclear membrane, Mitochondria Expressed in all thyroid gland: 18.8 MRPS15 FLJ11564 ENSG00000116898 Mitochondrial ribosomal protein S15 1 36455718-36464437 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA028100, HPA028134 Supportive Supportive Mitochondria, Nuclear membrane, Cytoplasm Expressed in all testis: 110.0 MRPS16 CGI-132 ENSG00000182180 Mitochondrial ribosomal protein S16 10 73248843-73252693 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA050081, HPA054538 Supportive Supportive Cytoplasm, Mitochondria Expressed in all colon: 25.8 MRPS17 HSPC011, MRP-S17, RPMS17 ENSG00000239789 Mitochondrial ribosomal protein S17 7 55951819-55956501 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA047159 Uncertain Expressed in all fallopian tube: 10.1 MRPS18A FLJ10548, MRPS18-3 ENSG00000096080 Mitochondrial ribosomal protein S18A 6 43671303-43687791 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA035450, HPA035451 Uncertain Expressed in all rectum: 41.8 MRPS18B C6orf14, HSPC183, MRPS18-2, PTD017 ENSG00000204568 Mitochondrial ribosomal protein S18B 6 30617709-30626395 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA043485, HPA050334 Supportive Supportive Mitochondria, Nucleus but not nucleoli, Cell Junctions Expressed in all fallopian tube: 61.6 MRPS18C CGI-134, FLJ11146, FLJ22967, MRPS18-1 ENSG00000163319 Mitochondrial ribosomal protein S18C 4 83455932-83469735 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA050404 Uncertain Expressed in all esophagus: 16.4 MRPS2 CGI-91 ENSG00000122140 Mitochondrial ribosomal protein S2 9 135499984-135504673 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA029487, HPA057261 Uncertain Supportive Mitochondria Expressed in all fallopian tube: 36.4 MRPS22 C3orf5, GIBT, GK002, MRP-S22 ENSG00000175110 Mitochondrial ribosomal protein S22 3 139005806-139357223 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA006083, HPA007830 Supportive Supportive Mitochondria Expressed in all adrenal gland: 50.2 MRPS23 CGI-138, HSPC329, MRP-S23 ENSG00000181610 Mitochondrial ribosomal protein S23 17 57834781-57850056 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA023453 Supportive Supportive Nuclear membrane, Mitochondria Expressed in all heart muscle: 36.6 MRPS24 HSPC335, MRP-S24 ENSG00000062582 Mitochondrial ribosomal protein S24 7 43866558-43869893 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA020983 Uncertain Uncertain Vesicles, Nucleus but not nucleoli Expressed in all skeletal muscle: 104.2 MRPS25 DKFZp313H0817, FLJ00023, MRP-S25, RPMS25 ENSG00000131368 Mitochondrial ribosomal protein S25 3 15042460-15065335 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA043490 Uncertain Supportive Mitochondria Expressed in all testis: 20.7 MRPS26 C20orf193, dJ534B8.3, MRP-S13, MRP-S26, RPMS13 ENSG00000125901 Mitochondrial ribosomal protein S26 20 3045945-3048254 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA045472, HPA054610 Supportive Supportive Mitochondria Expressed in all prostate: 31.6 MRPS27 KIAA0264 ENSG00000113048 Mitochondrial ribosomal protein S27 5 72219409-72320646 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Expressed in all thyroid gland: 45.4 MRPS28 HSPC007, MRP-S28, MRPS35 ENSG00000147586 Mitochondrial ribosomal protein S28 8 79918717-80030289 Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA027202 Uncertain Supportive Mitochondria Expressed in all heart muscle: 129.2 MRPS30 PAP, PDCD9 ENSG00000112996 Mitochondrial ribosomal protein S30 5 44808925-44820428 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA018686, HPA021149 Supportive Supportive Nucleus but not nucleoli, Cytoplasm Expressed in all bone marrow: 21.0 MRPS31 IMOGN38 ENSG00000102738 Mitochondrial ribosomal protein S31 13 40729135-40771173 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA039083, HPA046344 Supportive Supportive Mitochondria, Nucleoli Expressed in all tonsil: 20.0 MRPS33 CGI-139 ENSG00000090263 Mitochondrial ribosomal protein S33 7 141006054-141015228 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA030425 Uncertain Expressed in all rectum: 74.8 MRPS34 MGC2616, MRP-S12 ENSG00000074071 Mitochondrial ribosomal protein S34 16 1771890-1773155 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA042112 Supportive Supportive Mitochondria Expressed in all stomach: 21.1 MRPS35 MDS023, MRPS28 ENSG00000061794 Mitochondrial ribosomal protein S35 12 27710773-27756295 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA038513 Supportive Supportive Mitochondria, Cytoplasm Expressed in all rectum: 50.4 MRPS36 DC47, MRP-S36 ENSG00000134056 Mitochondrial ribosomal protein S36 5 69217760-69230129 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA035802, HPA056795 Supportive Supportive Mitochondria Expressed in all kidney: 21.1 MRPS5 MRP-S5, S5mt ENSG00000144029 Mitochondrial ribosomal protein S5 2 95087207-95149434 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA055765 Uncertain Supportive Mitochondria Expressed in all rectum: 26.8 MRPS6 C21orf101, MRP-S6, RPMS6 ENSG00000243927 Mitochondrial ribosomal protein S6 21 34073224-34143034 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA007861, HPA049676 Uncertain Expressed in all kidney: 92.4 MRPS7 MRP-S, RP-S7, RPMS7 ENSG00000125445 Mitochondrial ribosomal protein S7 17 75261674-75266373 Mitochondrial proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA022522, HPA023007 Supportive Uncertain Mitochondria Expressed in all heart muscle: 50.9 MRPS9 MRP-S9, RPMS9, S9mt ENSG00000135972 Mitochondrial ribosomal protein S9 2 105037983-105099960 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Ribosomal proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA043476, HPA048479 Supportive Supportive Mitochondria Expressed in all heart muscle: 31.7 MRRF RRF ENSG00000148187 Mitochondrial ribosome recycling factor 9 122264603-122323464 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA047177, HPA049987 Supportive Uncertain Cytoskeleton (Microtubules), Cytoskeleton (Cytokinetic bridge) Expressed in all rectum: 20.5 MRS2 MRS2L ENSG00000124532 MRS2 magnesium transporter 6 24402908-24426194 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA017642 Uncertain Expressed in all heart muscle: 17.5 MSRB2 CBS-1, CBS1, CGI-131, MSRB, PILB ENSG00000148450 Methionine sulfoxide reductase B2 10 23095506-23122013 Mitochondrial proteins, Predicted secreted proteins Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA027933 Uncertain Expressed in all heart muscle: 23.3 MSRB3 DFNB74, DKFZp686C1178, FLJ36866 ENSG00000174099 Methionine sulfoxide reductase B3 12 65278643-65488244 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA014432 Uncertain Expressed in all smooth muscle: 128.8 MSTO1 FLJ10504, LST005, misato, MST ENSG00000125459 Misato 1, mitochondrial distribution and morphology regulator 1 155610205-155614967 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA005899, HPA005914 Uncertain Uncertain Cytoplasm, Nuclear membrane Expressed in all thyroid gland: 9.1 MT-ATP6 ATP6, ATPase-6, MTATP6, RP, Su6m ENSG00000198899 Mitochondrially encoded ATP synthase 6 MT 8527-9207 Disease related genes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Expressed in all heart muscle: 43491.1 MT-ATP8 A6L, ATP8, MTATP8 ENSG00000228253 Mitochondrially encoded ATP synthase 8 MT 8366-8572 Disease related genes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA053976 Uncertain Uncertain Nucleoli, Nucleus, Mitochondria Expressed in all heart muscle: 311385.0 MT-CO1 COI, COX1, MTCO1 ENSG00000198804 Mitochondrially encoded cytochrome c oxidase I MT 5904-7445 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB016241, HPA069328 Supportive Supportive Mitochondria Expressed in all heart muscle: 59869.8 MT-CO2 CO2, COX2, MTCO2 ENSG00000198712 Mitochondrially encoded cytochrome c oxidase II MT 7586-8269 Disease related genes, Mitochondrial proteins, Potential drug targets, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB016243, HPA051505, HPA054758 Supportive Expressed in all heart muscle: 34069.8 MT-CO3 CO3, COIII, COX3, MTCO3 ENSG00000198938 Mitochondrially encoded cytochrome c oxidase III MT 9207-9990 Disease related genes, Mitochondrial proteins, Potential drug targets, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA042788 Uncertain Uncertain Nucleus but not nucleoli Expressed in all heart muscle: 46369.1 MT-CYB COB, CYTB, MTCYB, UQCR3 ENSG00000198727 Mitochondrially encoded cytochrome b MT 14747-15887 Disease related genes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level CAB032215, HPA068400 Uncertain Uncertain Mitochondria Expressed in all heart muscle: 19682.5 MT-ND1 MTND1, NAD1, ND1 ENSG00000198888 Mitochondrially encoded NADH dehydrogenase 1 MT 3307-4262 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level CAB033779 Uncertain Expressed in all heart muscle: 18489.0 MT-ND2 MTND2, NAD2, ND2 ENSG00000198763 Mitochondrially encoded NADH dehydrogenase 2 MT 4470-5511 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Expressed in all heart muscle: 20761.4 MT-ND3 MTND3, NAD3, ND3 ENSG00000198840 Mitochondrially encoded NADH dehydrogenase 3 MT 10059-10404 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA063296 Supportive Uncertain Cytoplasm Expressed in all heart muscle: 39294.6 MT-ND4 LHON, MTND4, NAD4, ND4 ENSG00000198886 Mitochondrially encoded NADH dehydrogenase 4 MT 10760-12137 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA053928 Uncertain Expressed in all heart muscle: 33482.1 MT-ND4L MTND4L, NAD4L, ND4L ENSG00000212907 Mitochondrially encoded NADH dehydrogenase 4L MT 10470-10766 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Expressed in all heart muscle: 34766.6 MT-ND5 MTND5, NAD5, ND5 ENSG00000198786 Mitochondrially encoded NADH dehydrogenase 5 MT 12337-14148 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Expressed in all heart muscle: 10648.7 MT-ND6 MTND6, NAD6, ND6 ENSG00000198695 Mitochondrially encoded NADH dehydrogenase 6 MT 14149-14673 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Expressed in all heart muscle: 16912.8 MTCH1 CGI-64, PSAP, SLC25A49 ENSG00000137409 Mitochondrial carrier 1 6 36968141-36986298 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA015971 Uncertain Expressed in all thyroid gland: 343.9 MTCH2 SLC25A50 ENSG00000109919 Mitochondrial carrier 2 11 47617315-47642623 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA038385, HPA038390 Uncertain Supportive Mitochondria Expressed in all testis: 67.3 MTERF1 MTERF ENSG00000127989 Mitochondrial transcription termination factor 1 7 91692008-91880720 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA044894, HPA069560 Uncertain Supportive Mitochondria Expressed in all lymph node: 11.7 MTERF2 FLJ14062, MTERFD3 ENSG00000120832 Mitochondrial transcription termination factor 2 12 106977291-106987166 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA003526 Uncertain Expressed in all adrenal gland: 18.3 MTERF3 CGI-12, FLJ10939, MTERFD1 ENSG00000156469 Mitochondrial transcription termination factor 3 8 96239398-96261610 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA002966 Uncertain Supportive Nucleus but not nucleoli, Mitochondria Expressed in all tonsil: 14.0 MTFMT FMT1 ENSG00000103707 Mitochondrial methionyl-tRNA formyltransferase 15 65001512-65029639 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA040710 Uncertain Uncertain Nucleus but not nucleoli, Cytoplasm Mixed smooth muscle: 1.7 MTFP1 HSPC242, MTP18 ENSG00000242114 Mitochondrial fission process 1 22 30425530-30429053 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Expressed in all lymph node: 12.3 MTFR1 CHPPR, FAM54A2, KIAA0009 ENSG00000066855 Mitochondrial fission regulator 1 8 65644734-65771261 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA023152, HPA056120 Uncertain Supportive Mitochondria, Cytoplasm Expressed in all kidney: 19.5 MTG1 GTPBP7 ENSG00000148824 Mitochondrial ribosome-associated GTPase 1 10 133394094-133421307 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA037826, HPA037827 Uncertain Expressed in all testis: 20.4 MTG2 dJ1005F21.2, FLJ10741, GTPBP5, ObgH1 ENSG00000101181 Mitochondrial ribosome-associated GTPase 2 20 62183029-62203568 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA047379 Uncertain Expressed in all prostate: 10.0 MTHFD1L DKFZP586G1517, FLJ21145, FTHFSDC1 ENSG00000120254 Methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 1-like 6 150865549-151101887 Enzymes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA015006, HPA029040, HPA029041, HPA050052 Uncertain Mixed placenta: 12.2 MTHFD2 ENSG00000065911 Methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 2, methenyltetrahydrofolate cyclohydrolase 2 74198562-74217565 Enzymes, Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB003684, HPA049657 Supportive Uncertain Expressed in all appendix: 29.0 MTIF2 IF-2mt ENSG00000085760 Mitochondrial translational initiation factor 2 2 55236595-55269347 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA006021, HPA061422 Uncertain Supportive Mitochondria Expressed in all rectum: 25.8 MTIF3 IF-3mt, IF3(mt) ENSG00000122033 Mitochondrial translational initiation factor 3 13 27435643-27450591 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA039791 Uncertain Supportive Mitochondria, Nucleus but not nucleoli Expressed in all testis: 49.3 MTO1 ENSG00000135297 Mitochondrial tRNA translation optimization 1 6 73461578-73509236 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA030230, HPA030232 Supportive Uncertain Nucleus but not nucleoli, Cytoplasm Expressed in all lymph node: 9.8 MTPAP FLJ10486, mtPAP, PAPD1, SPAX4 ENSG00000107951 Mitochondrial poly(A) polymerase 10 30309801-30374448 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA038620, HPA058232 Uncertain Supportive Mitochondria Expressed in all bone marrow: 14.2 MTRF1 MGC47721, MTTRF1, RF1 ENSG00000120662 Mitochondrial translational release factor 1 13 41216369-41263577 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA043316 Uncertain Expressed in all testis: 12.3 MTRF1L ENSG00000112031 Mitochondrial translational release factor 1-like 6 152987362-153002685 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA036367 Uncertain Mixed duodenum: 5.5 MTRR cblE ENSG00000124275 5-methyltetrahydrofolate-homocysteine methyltransferase reductase 5 7851186-7906025 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA038113 Supportive Uncertain Nucleus but not nucleoli, Cytoplasm, Cytoskeleton (Intermediate filaments) Mixed kidney: 11.9 MTUS1 ATBP, ATIP1, DKFZp586D1519, FLJ14295, ICIS, KIAA1288, MP44, MTSG1 ENSG00000129422 Microtubule associated tumor suppressor 1 8 17643795-17800917 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA067903, HPA069795 Supportive Nucleoli, Cytoskeleton (Microtubules) Mixed placenta: 45.2 MTX1 MTX, MTXN ENSG00000173171 Metaxin 1 1 155208699-155213824 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA011543 Uncertain Supportive Mitochondria Expressed in all testis: 28.0 MTX2 ENSG00000128654 Metaxin 2 2 176269395-176338025 Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA031550, HPA031551, HPA031552 Supportive Expressed in all testis: 54.1 MTX3 ENSG00000177034 Metaxin 3 5 79976731-79991262 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA047858, HPA062061 Uncertain Uncertain Mitochondria Expressed in all ovary: 13.2 MUL1 C1orf166, FLJ12875, GIDE, MAPL, MULAN, RNF218 ENSG00000090432 Mitochondrial E3 ubiquitin protein ligase 1 1 20499448-20508161 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA017681, HPA026827 Uncertain Supportive Nucleus but not nucleoli, Cytoplasm, Mitochondria Expressed in all fallopian tube: 20.6 MUT ENSG00000146085 Methylmalonyl CoA mutase 6 49430360-49463191 Disease related genes, Enzymes, FDA approved drug targets, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA035971, HPA035972 Supportive Uncertain Cytoplasm, Mitochondria Expressed in all liver: 63.5 MYCBP AMY-1 ENSG00000214114 MYC binding protein 1 38862964-38874495 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041188 Supportive Expressed in all fallopian tube: 17.3 NAGS AGAS, ARGA, NAT7 ENSG00000161653 N-acetylglutamate synthase 17 44004546-44009063 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Tissue enhanced 0 duodenum: 9.9;small intestine: 7.8 kidney: 4.8 NARS2 FLJ23441, SLM5 ENSG00000137513 Asparaginyl-tRNA synthetase 2, mitochondrial (putative) 11 78435961-78574874 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA026793 Supportive Uncertain Nucleus but not nucleoli, Mitochondria, Cytoplasm Expressed in all fallopian tube: 14.9 NDUFA1 CI-MWFE, MWFE ENSG00000125356 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa X 119871487-119876662 Disease related genes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA029768, HPA054359 Supportive Supportive Cytoplasm, Mitochondria Expressed in all heart muscle: 169.8 NDUFA10 CI-42k ENSG00000130414 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa 2 239892450-240025402 Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA059529 Supportive Mitochondria Expressed in all heart muscle: 107.1 NDUFA11 B14.7 ENSG00000174886 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 11, 14.7kDa 19 5891276-5904006 Disease related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Expressed in all heart muscle: 272.8 NDUFA12 B17.2, DAP13 ENSG00000184752 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 12 94897055-95003770 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA039903 Supportive Expressed in all heart muscle: 160.6 NDUFA13 B16.6, CDA016, CGI-39, GRIM-19, GRIM19 ENSG00000186010 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 13 19 19515736-19529054 Disease related genes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041213 Supportive Supportive Mitochondria Expressed in all heart muscle: 177.0 NDUFA2 B8 ENSG00000131495 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa 5 140638740-140647785 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA035933 Uncertain Expressed in all kidney: 82.1 NDUFA3 B9 ENSG00000170906 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa 19 54102728-54109257 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA046976 Supportive Expressed in all skeletal muscle: 144.1 NDUFA4 CI-9k, MLRQ ENSG00000189043 NDUFA4, mitochondrial complex associated 7 10931951-10940256 Disease related genes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA055323 Uncertain Mitochondria Expressed in all heart muscle: 98.9 NDUFA4L2 FLJ26118, NUOMS ENSG00000185633 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4-like 2 12 57234903-57240715 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA055323 Uncertain Mitochondria Tissue enhanced 0 esophagus: 107.2;skin: 115.9 placenta: 80.1 NDUFA5 B13, CI-13kB, CI-13KD-B, NUFM, UQOR13 ENSG00000128609 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5 7 123536997-123558255 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA043175 Supportive Expressed in all thyroid gland: 126.8 NDUFA6 B14, CI-B14, LYRM6, NADHB14 ENSG00000184983 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa 22 42085525-42090955 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA056934 Uncertain Expressed in all heart muscle: 112.1 NDUFA7 B14.5a ENSG00000267855 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 7, 14.5kDa 19 8308768-8321396 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA059251 Uncertain Supportive Mitochondria Expressed in all heart muscle: 55.8 NDUFA8 MGC793, PGIV ENSG00000119421 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa 9 122144058-122159819 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041510, HPA041600 Supportive Supportive Mitochondria Expressed in all heart muscle: 190.1 NDUFA9 CI-39k, NDUFS2L, SDR22E1 ENSG00000139180 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa 12 4649095-4694317 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA042268, HPA073212 Supportive Supportive Nucleus but not nucleoli, Mitochondria Expressed in all skeletal muscle: 28.0 NDUFAB1 ACP, FASN2A, SDAP ENSG00000004779 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa 16 23581002-23596356 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA054364 Uncertain Expressed in all heart muscle: 147.9 NDUFAF1 CGI-65, CIA30 ENSG00000137806 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1 15 41387349-41402519 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA039933, HPA040064 Supportive Supportive Cytoplasm Expressed in all adrenal gland: 26.3 NDUFAF2 B17.2L, mimitin, MMTN, NDUFA12L ENSG00000164182 NADH dehydrogenase (ubiquinone) complex I, assembly factor 2 5 60945129-61153037 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA048082, HPA054776 Supportive Supportive Mitochondria Expressed in all thyroid gland: 21.7 NDUFAF4 bA22L21.1, C6orf66, HRPAP20, HSPC125, My013 ENSG00000123545 NADH dehydrogenase (ubiquinone) complex I, assembly factor 4 6 96889313-96897881 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA046560 Uncertain Supportive Mitochondria Expressed in all cerebral cortex: 14.8 NDUFAF7 C2orf56, MidA, PRO1853 ENSG00000003509 NADH dehydrogenase (ubiquinone) complex I, assembly factor 7 2 37231631-37253403 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA045217 Uncertain Expressed in all testis: 27.9 NDUFB1 CI-MNLL, MNLL ENSG00000183648 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa 14 92116122-92121917 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA047940, HPA063737 Uncertain Supportive Nucleus but not nucleoli, Mitochondria Expressed in all heart muscle: 328.2 NDUFB10 PDSW ENSG00000140990 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa 16 1959508-1961975 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Expressed in all skeletal muscle: 338.5 NDUFB11 ESSS, Np15, NP17.3 ENSG00000147123 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa X 47142216-47145504 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA030367 Supportive Supportive Mitochondria Expressed in all skeletal muscle: 92.0 NDUFB2 AGGG, CI-AGGG ENSG00000090266 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa 7 140690777-140722790 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA051377 Uncertain Expressed in all heart muscle: 322.9 NDUFB3 B12 ENSG00000119013 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa 2 201071433-201085750 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA034596 Uncertain Expressed in all skeletal muscle: 135.5 NDUFB4 B15 ENSG00000065518 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa 3 120596309-120602500 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA051739, HPA064441 Supportive Supportive Nucleus, Mitochondria, Nuclear membrane Expressed in all esophagus: 206.3 NDUFB5 CI-SGDH, MGC12314, SGDH ENSG00000136521 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa 3 179604690-179627647 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA005640 Supportive Supportive Mitochondria, Nucleus but not nucleoli Expressed in all heart muscle: 114.0 NDUFB6 B17, CI ENSG00000165264 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa 9 32552999-32573184 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA044001, HPA053334 Supportive Supportive Mitochondria Expressed in all heart muscle: 55.1 NDUFB7 B18, CI-B18, MGC2480 ENSG00000099795 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa 19 14566078-14572062 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA002817 Uncertain Expressed in all skeletal muscle: 189.1 NDUFB8 ASHI, CI-ASHI ENSG00000166136 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa 10 100523740-100530000 Mitochondrial proteins, Plasma proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA003886 Supportive Supportive Mitochondria Expressed in all heart muscle: 260.9 NDUFB9 B22, LYRM3, UQOR22 ENSG00000147684 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa 8 124539103-124568510 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA042768 Uncertain Supportive Mitochondria Expressed in all skeletal muscle: 310.3 NDUFC1 KFYI ENSG00000109390 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa 4 139266880-139302551 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA044556 Uncertain Supportive Mitochondria Expressed in all skeletal muscle: 68.8 NDUFC2 B14.5b, HLC-1 ENSG00000151366 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa 11 78068304-78080219 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA038873, HPA056195 Uncertain Expressed in all thyroid gland: 232.4 NDUFS1 CI-75k ENSG00000023228 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase) 2 206114817-206159603 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA064605 Supportive Mitochondria Expressed in all heart muscle: 117.7 NDUFS2 CI-49 ENSG00000158864 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase) 1 161197104-161214395 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA055140, HPA061953 Supportive Supportive Mitochondria, Nucleus but not nucleoli Expressed in all heart muscle: 111.6 NDUFS3 CI-30 ENSG00000213619 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase) 11 47565336-47584562 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA004484 Uncertain Supportive Mitochondria, Nucleus Expressed in all skeletal muscle: 102.8 NDUFS4 AQDQ, CI-18 ENSG00000164258 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase) 5 53560633-53683340 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA003884 Supportive Supportive Mitochondria Expressed in all heart muscle: 125.1 NDUFS5 CI-15k ENSG00000168653 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase) 1 39026318-39034636 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA042582 Supportive Uncertain Cytoplasm, Nucleus Expressed in all heart muscle: 407.8 NDUFS6 CI-13kA ENSG00000145494 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase) 5 1801400-1816605 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA064221 Supportive Expressed in all skeletal muscle: 76.4 NDUFS7 CI-20, FLJ45860, FLJ46880, PSST ENSG00000115286 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase) 19 1383527-1395589 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Expressed in all skeletal muscle: 90.8 NDUFS8 CI-23k, TYKY ENSG00000110717 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase) 11 68030617-68036644 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA018524 Uncertain Supportive Mitochondria Expressed in all skeletal muscle: 104.4 NDUFV1 CI-51K ENSG00000167792 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa 11 67606852-67612535 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA045211 Uncertain Expressed in all heart muscle: 151.1 NDUFV2 CI-24k ENSG00000178127 NADH dehydrogenase (ubiquinone) flavoprotein 2, 24kDa 18 9102630-9134345 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA003404 Supportive Uncertain Expressed in all skeletal muscle: 46.2 NDUFV3 CI-10k ENSG00000160194 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa 21 42879644-42913304 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA019791, HPA020463, HPA030427, CAB034142 Supportive Supportive Mitochondria Expressed in all skeletal muscle: 20.0 NFS1 IscS, NifS ENSG00000244005 NFS1 cysteine desulfurase 20 35668055-35699359 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB034314, HPA051801, HPA054755 Supportive Supportive Nucleus but not nucleoli, Cytoplasm, Vesicles Expressed in all kidney: 24.5 NFU1 CGI-33, HIRIP5, NifU, NIFUC ENSG00000169599 NFU1 iron-sulfur cluster scaffold 2 69395750-69437628 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA035825, HPA035826 Uncertain Supportive Cytoplasm, Nucleus but not nucleoli Expressed in all adipose tissue: 49.3 NLN AGTBP, KIAA1226 ENSG00000123213 Neurolysin (metallopeptidase M3 family) 5 65722196-65871725 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA031862 Uncertain Uncertain Mitochondria Mixed liver: 4.2 NLRP5 CLR19.8, MATER, NALP5, PAN11, PYPAF8 ENSG00000171487 NLR family, pyrin domain containing 5 19 55999726-56061813 Mitochondrial proteins, Predicted secreted proteins Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA056271 Uncertain Not detected testis: 0.2 NME4 NDPKD, nm23-H4, NM23H4 ENSG00000103202 NME/NM23 nucleoside diphosphate kinase 4 16 396725-410367 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB045996, CAB045997, HPA072588 Supportive Supportive Mitochondria Expressed in all prostate: 100.3 NNT ENSG00000112992 Nicotinamide nucleotide transhydrogenase 5 43602692-43707405 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA004829, CAB004975 Supportive Supportive Mitochondria Expressed in all heart muscle: 109.4 NT5M dNT-2, dNT2, mdN ENSG00000205309 5',3'-nucleotidase, mitochondrial 17 17303335-17347663 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level HPA043777 Uncertain Mixed testis: 3.8 NUDT17 FLJ34433 ENSG00000186364 Nudix (nucleoside diphosphate linked moiety X)-type motif 17 1 145845629-145848953 Mitochondrial proteins, Predicted intracellular proteins Evidence at transcript level Evidence at transcript level Evidence at transcript level HPA030145 Uncertain Uncertain Cytoplasm, Centrosome Mixed lymph node: 3.0 NUDT19 RP2 ENSG00000213965 Nudix (nucleoside diphosphate linked moiety X)-type motif 19 19 32691961-32713796 Mitochondrial proteins, Predicted secreted proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Expressed in all adrenal gland: 8.1 NUDT8 FLJ41567 ENSG00000167799 Nudix (nucleoside diphosphate linked moiety X)-type motif 8 11 67627938-67629930 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA041252, HPA041466 Supportive Uncertain Nucleoli, Cytoplasm Expressed in all heart muscle: 16.1 NUDT9 MGC3037 ENSG00000170502 Nudix (nucleoside diphosphate linked moiety X)-type motif 9 4 87422582-87459454 Enzymes, Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA036917, HPA044866 Uncertain Expressed in all kidney: 30.1 OAS1 IFI-4, OIAS, OIASI ENSG00000089127 2'-5'-oligoadenylate synthetase 1, 40/46kDa 12 112906777-112932185 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA003657, CAB021104 Uncertain Uncertain Cytoplasm Expressed in all spleen: 53.9 OAS2 ENSG00000111335 2'-5'-oligoadenylate synthetase 2, 69/71kDa 12 112978395-113011723 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB024984, HPA045947 Uncertain Uncertain Nucleus but not nucleoli, Cytoplasm Mixed spleen: 39.6 OAT HOGA ENSG00000065154 Ornithine aminotransferase 10 124397303-124418976 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB033576, HPA040098, HPA064742 Supportive Supportive Nucleus but not nucleoli, Mitochondria Group enriched 6 duodenum: 553.9;small intestine: 560.5 salivary gland: 99.5 OGDH E1k ENSG00000105953 Oxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide) 7 44606572-44709066 Citric acid cycle related proteins, Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA019514, HPA020347 Supportive Supportive Mitochondria Expressed in all heart muscle: 120.2 OGDHL FLJ10851 ENSG00000197444 Oxoglutarate dehydrogenase-like 10 49734643-49762379 Citric acid cycle related proteins, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA052497 Uncertain Uncertain Nucleoli, Nucleus, Cytoplasm Tissue enhanced 0 kidney: 121.5 liver: 30.9 OGG1 HMMH, HOGG1, MUTM, OGH1 ENSG00000114026 8-oxoguanine DNA glycosylase 3 9749944-9788219 Cancer-related genes, Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA027514, CAB047301 Supportive Supportive Nucleus but not nucleoli Expressed in all kidney: 21.4 OMA1 FLJ33782, MPRP-1, YKR087C, ZMPOMA1 ENSG00000162600 OMA1 zinc metallopeptidase 1 58415384-58546802 Cancer-related genes, Enzymes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA055120 Uncertain Uncertain Nucleus but not nucleoli, Mitochondria Expressed in all fallopian tube: 16.2 OPA1 FLJ12460, KIAA0567, MGM1, NPG, NTG ENSG00000198836 Optic atrophy 1 (autosomal dominant) 3 193593144-193697823 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA036926, HPA036927 Supportive Supportive Nucleus but not nucleoli, Mitochondria Expressed in all cerebral cortex: 28.8 OPA3 FLJ22187, MGA3 ENSG00000125741 Optic atrophy 3 (autosomal recessive, with chorea and spastic paraplegia) 19 45527427-45602212 Disease related genes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA044881 Uncertain Uncertain Cytoplasm, Nucleus but not nucleoli Expressed in all kidney: 6.3 OTC ENSG00000036473 Ornithine carbamoyltransferase X 38352545-38421450 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA000243, HPA000570 Supportive Supportive Mitochondria Group enriched 22 duodenum: 82.1;liver: 114.9;small intestine: 64.4 colon: 3.9 OXA1L MGC133129, OXA1 ENSG00000155463 Oxidase (cytochrome c) assembly 1-like 14 22766522-22773041 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA003531 Uncertain Supportive Mitochondria Expressed in all tonsil: 85.0 OXCT1 OXCT, SCOT ENSG00000083720 3-oxoacid CoA transferase 1 5 41730065-41870519 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA012047, HPA061425 Supportive Supportive Mitochondria Tissue enhanced 0 heart muscle: 144.9 cerebral cortex: 52.3 OXCT2 FKSG25, FLJ00030, SCOT-T ENSG00000198754 3-oxoacid CoA transferase 2 1 39769523-39771348 Enzymes, Mitochondrial proteins, Predicted secreted proteins Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA053950 Uncertain Tissue enriched 10 testis: 19.9 heart muscle: 2.0 OXR1 TLDC3 ENSG00000164830 Oxidation resistance 1 8 106270178-106752694 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA027375, HPA027380, HPA027395 Supportive Supportive Vesicles Expressed in all cerebral cortex: 54.0 OXSM FASN2D, FLJ20604, KS ENSG00000151093 3-oxoacyl-ACP synthase, mitochondrial 3 25782917-25794534 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA021293, HPA021300, HPA021337 Supportive Supportive Cytoplasm, Mitochondria Expressed in all rectum: 9.5 PACS2 KIAA0602, PACS1L ENSG00000179364 Phosphofurin acidic cluster sorting protein 2 14 105300563-105398147 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA001423 Uncertain Expressed in all cerebral cortex: 29.6 PAM16 Magmas, Tim16, TIMM16 ENSG00000217930 Presequence translocase-associated motor 16 homolog (S. cerevisiae) 16 4331549-4355607 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level HPA062721 Uncertain Nucleus but not nucleoli, Mitochondria, Cytoskeleton (Microtubules) Expressed in all skeletal muscle: 22.9 PANK2 C20orf48, FLJ11729, HARP, HSS, NBIA1, PKAN ENSG00000125779 Pantothenate kinase 2 20 3888839-3929882 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA008440, HPA021795 Uncertain Supportive Cytoplasm Expressed in all testis: 25.2 PARL PRO2207, PSARL, PSARL1, RHBDS1 ENSG00000175193 Presenilin associated, rhomboid-like 3 183829385-183884933 Enzymes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA019545 Uncertain Supportive Mitochondria Expressed in all rectum: 38.9 PARS2 DKFZp727A071 ENSG00000162396 Prolyl-tRNA synthetase 2, mitochondrial (putative) 1 54756898-54764514 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA028314, HPA028518 Uncertain Uncertain Centrosome, Nucleus Mixed fallopian tube: 4.6 PC PCB ENSG00000173599 Pyruvate carboxylase 11 66848233-66958376 Citric acid cycle related proteins, Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB033742, HPA043922, HPA058765 Supportive Supportive Mitochondria Expressed in all adipose tissue: 40.0 PCCA ENSG00000175198 Propionyl CoA carboxylase, alpha polypeptide 13 100089015-100530435 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041716, HPA047792 Supportive Expressed in all kidney: 98.1 PCCB ENSG00000114054 Propionyl CoA carboxylase, beta polypeptide 3 136250306-136337896 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA036939, HPA036940 Supportive Expressed in all liver: 56.7 PCK2 PEPCK, PEPCK2 ENSG00000100889 Phosphoenolpyruvate carboxykinase 2 (mitochondrial) 14 24094053-24110598 Citric acid cycle related proteins, Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB018734, HPA051162, HPA053502 Supportive Supportive Mitochondria Group enriched 6 duodenum: 263.6;kidney: 171.2;liver: 169.3;small intestine: 186.2 colon: 35.3 PDF ENSG00000258429 Peptide deformylase (mitochondrial) 16 69328621-69330595 Enzymes, Mitochondrial proteins, Predicted secreted proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA063409 Uncertain Expressed in all kidney: 6.4 PDHA1 PDHA ENSG00000131828 Pyruvate dehydrogenase (lipoamide) alpha 1 X 19343893-19361705 Citric acid cycle related proteins, Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA047487, HPA047864, HPA063053 Uncertain Expressed in all heart muscle: 185.4 PDHA2 PDHAL ENSG00000163114 Pyruvate dehydrogenase (lipoamide) alpha 2 4 95840019-95841474 Citric acid cycle related proteins, Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA047487, HPA047864, HPA063053 Uncertain Tissue enriched 492 testis: 49.2 adipose tissue: 0.0 PDHB ENSG00000168291 Pyruvate dehydrogenase (lipoamide) beta 3 58427630-58433857 Citric acid cycle related proteins, Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB033794, HPA036744, HPA036745 Supportive Supportive Mitochondria, Nucleus but not nucleoli Expressed in all heart muscle: 93.5 PDHX DLDBP, E3BP, OPDX, PDX1, proX ENSG00000110435 Pyruvate dehydrogenase complex, component X 11 34915829-35020591 Disease related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA038484, HPA038485 Supportive Uncertain Nucleus, Plasma membrane, Mitochondria Expressed in all heart muscle: 43.5 PDK1 ENSG00000152256 Pyruvate dehydrogenase kinase, isozyme 1 2 172555373-172608669 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level CAB017554, HPA027376 Uncertain Expressed in all heart muscle: 15.2 PDK2 PDHK2 ENSG00000005882 Pyruvate dehydrogenase kinase, isozyme 2 17 50094737-50112152 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA008287 Supportive Supportive Nucleus but not nucleoli, Mitochondria Expressed in all skeletal muscle: 55.3 PDK3 ENSG00000067992 Pyruvate dehydrogenase kinase, isozyme 3 X 24465221-24539837 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA046583 Uncertain Mixed testis: 12.2 PDK4 ENSG00000004799 Pyruvate dehydrogenase kinase, isozyme 4 7 95583499-95596491 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA056731 Uncertain Expressed in all adipose tissue: 317.0 PDP1 PDH, PDP, PPM2C ENSG00000164951 Pyruvate dehyrogenase phosphatase catalytic subunit 1 8 93857807-93926066 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA018483, HPA019081, HPA021152 Uncertain Supportive Nucleus but not nucleoli, Cytoplasm, Mitochondria Expressed in all adrenal gland: 47.3 PDP2 KIAA1348, PPM2C2 ENSG00000172840 Pyruvate dehyrogenase phosphatase catalytic subunit 2 16 66878589-66895754 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA019950, HPA062059 Uncertain Supportive Mitochondria Expressed in all thyroid gland: 8.1 PDPR PDP3 ENSG00000090857 Pyruvate dehydrogenase phosphatase regulatory subunit 16 70113626-70162537 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA048092, HPA049143, HPA049815 Uncertain Supportive Cytoplasm Expressed in all testis: 15.7 PEMT PEMPT, PEMT2 ENSG00000133027 Phosphatidylethanolamine N-methyltransferase 17 17505563-17591708 Enzymes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA042375 Uncertain Uncertain Cytoplasm Expressed in all liver: 70.9 PGS1 DKFZP762M186 ENSG00000087157 Phosphatidylglycerophosphate synthase 1 17 78378640-78425114 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA022526 Uncertain Uncertain Vesicles, Cytoskeleton (Intermediate filaments), Cell Junctions Expressed in all lung: 18.8 PHB PHB1 ENSG00000167085 Prohibitin 17 49404049-49414905 Mitochondrial proteins, Plasma proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA003280 Supportive Supportive Mitochondria, Vesicles Expressed in all kidney: 128.4 PHB2 Bap37, BCAP37, p22, REA ENSG00000215021 Prohibitin 2 12 6965327-6970825 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB014889, CAB026335, HPA039874 Supportive Supportive Mitochondria Expressed in all ovary: 210.7 PHYKPL AGXT2L2, MGC15875 ENSG00000175309 5-phosphohydroxy-L-lysine phospho-lyase 5 178208497-178232791 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA036461, HPA063608 Uncertain Uncertain Mitochondria Expressed in all rectum: 16.3 PI4KB PI4K-BETA, pi4K92, PIK4CB ENSG00000143393 Phosphatidylinositol 4-kinase, catalytic, beta 1 151291797-151327715 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA006280, HPA006281, CAB022071 Uncertain Supportive Cytoplasm, Golgi apparatus Expressed in all fallopian tube: 47.6 PINK1 PARK6 ENSG00000158828 PTEN induced putative kinase 1 1 20633455-20651511 Cytoskeleton related proteins, Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level HPA001931, CAB026191 Uncertain Expressed in all skeletal muscle: 87.2 PISD dJ858B16.2, PSDC ENSG00000241878 Phosphatidylserine decarboxylase 22 31618491-31662432 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA031090, HPA031091 Supportive Uncertain Cytoplasm, Golgi apparatus Expressed in all adipose tissue: 23.0 PITRM1 hMP1, KIAA1104, MP1, PreP ENSG00000107959 Pitrilysin metallopeptidase 1 10 3137728-3172841 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA006753, HPA006754 Supportive Supportive Mitochondria Expressed in all testis: 39.4 PLGRKT AD025, C9orf46, FLJ14688, MDS030, Plg-RKT ENSG00000107020 Plasminogen receptor, C-terminal lysine transmembrane protein 9 5357973-5437878 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA008214, HPA011144 Supportive Expressed in all rectum: 50.3 PMAIP1 APR, NOXA ENSG00000141682 Phorbol-12-myristate-13-acetate-induced protein 1 18 59899948-59904306 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level HPA051063 Uncertain Uncertain Vesicles Tissue enhanced 0 bone marrow: 44.7 placenta: 12.7 PMPCA Alpha-MPP, INPP5E, KIAA0123 ENSG00000165688 Peptidase (mitochondrial processing) alpha 9 136410570-136423761 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA021648, HPA063735 Supportive Supportive Mitochondria Expressed in all heart muscle: 25.8 PMPCB MPPB, MPPP52 ENSG00000105819 Peptidase (mitochondrial processing) beta 7 103297422-103329511 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA040674 Uncertain Supportive Mitochondria Expressed in all lymph node: 31.5 PNKD BRP17, DKFZp564N1362, DYT8, FKSG19, FPD1, KIAA1184, KIPP1184, MGC31943, MR-1, PDC, PKND1, TAHCCP2 ENSG00000127838 Paroxysmal nonkinesigenic dyskinesia 2 218270392-218346793 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA010134, HPA017068 Supportive Supportive Mitochondria Expressed in all prostate: 65.3 PNPT1 DFNB70, old-35, OLD35, PNPase ENSG00000138035 Polyribonucleotide nucleotidyltransferase 1 2 55634063-55693910 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB033424, HPA034602, HPA034603 Supportive Supportive Mitochondria Expressed in all thyroid gland: 5.8 POLG POLG1, POLGA ENSG00000140521 Polymerase (DNA directed), gamma 15 89316303-89334861 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA056821 Uncertain Expressed in all lymph node: 16.5 POLG2 HP55, MTPOLB ENSG00000256525 Polymerase (DNA directed), gamma 2, accessory subunit 17 64477785-64497036 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB017030, HPA023202 Uncertain Supportive Nucleus, Mitochondria Expressed in all testis: 10.0 POLRMT APOLMT, h-mtRPOL, MTRNAP, MTRPOL ENSG00000099821 Polymerase (RNA) mitochondrial (DNA directed) 19 617223-633604 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA006366 Uncertain Supportive Mitochondria Expressed in all testis: 19.1 PPA2 FLJ20459 ENSG00000138777 Pyrophosphatase (inorganic) 2 4 105369077-105474081 Cancer-related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA030888, HPA031671, HPA031672 Uncertain Supportive Mitochondria, Nucleus Expressed in all kidney: 12.8 PPIF Cyp-D, hCyP3 ENSG00000108179 Peptidylprolyl isomerase F 10 79347469-79355337 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Expressed in all adrenal gland: 115.8 PPL ENSG00000118898 Periplakin 16 4882507-4960741 Cytoskeleton related proteins, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA042550, HPA059859 Supportive Group enriched 5 esophagus: 410.2;skin: 90.1 tonsil: 47.2 PPM1K BDP, DKFZp761G058, hPTMP, PP2Ckappa, PP2Cm ENSG00000163644 Protein phosphatase, Mg2+/Mn2+ dependent, 1K 4 88257620-88284769 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA020066, HPA020862, HPA023891 Uncertain Supportive Mitochondria Expressed in all heart muscle: 53.0 PPOX PPO, VP ENSG00000143224 Protoporphyrinogen oxidase 1 161166410-161178013 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA030123 Uncertain Uncertain Cytoplasm, Mitochondria Expressed in all fallopian tube: 23.7 PRDX3 AOP-1, AOP1, MER5, SP-22 ENSG00000165672 Peroxiredoxin 3 10 119167703-119178833 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB008656, HPA041488 Supportive Expressed in all adrenal gland: 295.5 PRDX5 ACR1, AOEB166, B166, MGC117264, MGC142283, MGC142285, PLP, PMP20, PRDX6, PRXV, SBBI10 ENSG00000126432 Peroxiredoxin 5 11 64318088-64321811 Enzymes, FDA approved drug targets, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB008661, HPA037915, HPA037916 Supportive Supportive Cytoplasm, Mitochondria Expressed in all fallopian tube: 377.8 PRELID1 CGI-106, PRELI, PX19 ENSG00000169230 PRELI domain containing 1 5 177303774-177306959 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA005701 Uncertain Supportive Mitochondria, Nucleus but not nucleoli Expressed in all colon: 30.0 PRODH HSPOX2, PIG6, PRODH1, PRODH2, TP53I6 ENSG00000100033 Proline dehydrogenase (oxidase) 1 22 18912777-18936553 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA020361 Uncertain Tissue enhanced 0 small intestine: 19.5 lung: 8.8 PTPMT1 DUSP23, MOSP, PLIP ENSG00000110536 Protein tyrosine phosphatase, mitochondrial 1 11 47565430-47573461 Enzymes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA040348, HPA043932 Uncertain Supportive Mitochondria Expressed in all testis: 48.6 PTRF cavin-1, CAVIN1 ENSG00000177469 Polymerase I and transcript release factor 17 42402452-42423517 Disease related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA049838 Supportive Expressed in all adipose tissue: 235.2 PTRH2 BIT1, CFAP37, CGI-147, PTH2 ENSG00000141378 Peptidyl-tRNA hydrolase 2 17 59674636-59707626 Enzymes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA012897 Supportive Supportive Mitochondria Expressed in all rectum: 17.4 PYCR1 P5C ENSG00000183010 Pyrroline-5-carboxylate reductase 1 17 81932384-81942412 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA047660 Uncertain Expressed in all salivary gland: 58.9 RAB11FIP5 GAF1, KIAA0857, pp75, RIP11 ENSG00000135631 RAB11 family interacting protein 5 (class I) 2 73073382-73156721 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA036406, HPA036407 Supportive Supportive Vesicles, Microtubule organizing center Tissue enhanced 0 testis: 23.1 spleen: 12.4 RAB32 ENSG00000118508 RAB32, member RAS oncogene family 6 146543693-146554965 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA025731 Uncertain Uncertain Cytoplasm Expressed in all bone marrow: 72.3 RAB40AL RAR2, RLGP ENSG00000102128 RAB40A, member RAS oncogene family-like X 102937250-102938962 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Tissue enhanced 0 esophagus: 0.5 prostate: 0.2 RARS2 DALRD2, dJ382I10.6, MGC14993, MGC23778, PRO1992, RARSL ENSG00000146282 Arginyl-tRNA synthetase 2, mitochondrial 6 87514378-87590003 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA039987, HPA042645 Uncertain Uncertain Cytoplasm, Nucleus Expressed in all adrenal gland: 30.5 RBFA C18orf22, FLJ21172, HsT169 ENSG00000101546 Ribosome binding factor A (putative) 18 80034358-80046397 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA040485, HPA041479 Supportive Supportive Mitochondria Expressed in all adipose tissue: 12.9 REEP1 C2orf23, FLJ13110, SPG31 ENSG00000068615 Receptor accessory protein 1 2 86213993-86338083 Disease related genes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA058061 Uncertain Tissue enhanced 0 testis: 47.6 cerebral cortex: 28.3 REXO2 CGI-114, DKFZP566E144, SFN ENSG00000076043 RNA exonuclease 2 11 114439386-114450279 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA038450, HPA038451 Supportive Supportive Mitochondria, Nucleoli, Focal Adhesions Expressed in all smooth muscle: 90.1 RHOT1 ARHT1, FLJ11040, MIRO-1 ENSG00000126858 Ras homolog family member T1 17 32142454-32253374 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA010687, CAB068223, CAB068224 Supportive Expressed in all adrenal gland: 24.1 RHOT2 ARHT2, C16orf39, MIRO-2 ENSG00000140983 Ras homolog family member T2 16 668086-674174 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA012624, HPA012895 Supportive Supportive Cytoplasm Expressed in all spleen: 22.9 RMDN3 FAM82A2, FAM82C, FLJ10579, PTPIP51, RMD3 ENSG00000137824 Regulator of microtubule dynamics 3 15 40735884-40755851 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA009975 Supportive Supportive Mitochondria Expressed in all small intestine: 37.1 RNASEL PRCA1, RNS4 ENSG00000135828 Ribonuclease L (2',5'-oligoisoadenylate synthetase-dependent) 1 182573634-182589256 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA002633, CAB010906 Supportive Supportive Cytoplasm Mixed ovary: 9.4 RSAD1 FLJ11164 ENSG00000136444 Radical S-adenosyl methionine domain containing 1 17 50478800-50485975 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA022436, HPA022967 Supportive Uncertain Cytoplasm, Nucleus but not nucleoli, Plasma membrane Expressed in all adrenal gland: 20.7 RTN4IP1 NIMP ENSG00000130347 Reticulon 4 interacting protein 1 6 106571971-106629487 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA036357 Uncertain Expressed in all heart muscle: 7.2 SAMM50 CGI-51, OMP85, TOB55, TRG-3, YNL026W ENSG00000100347 SAMM50 sorting and assembly machinery component 22 43955421-44010531 Mitochondrial proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA034537 Supportive Supportive Mitochondria Expressed in all skeletal muscle: 58.2 SARDH DMGDHL1, SDH ENSG00000123453 Sarcosine dehydrogenase 9 133663560-133739955 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA057267, HPA058086 Supportive Uncertain Mitochondria Group enriched 7 kidney: 14.6;liver: 38.3;pancreas: 11.2 salivary gland: 2.9 SARS2 FLJ20450, mtSerRS, SARS, SARSM, SerRSmt, SERS, SYS ENSG00000104835 Seryl-tRNA synthetase 2, mitochondrial 19 38915266-38930896 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA052730, HPA056957 Supportive Expressed in all thyroid gland: 10.4 SCO1 SCOD1 ENSG00000133028 SCO1 cytochrome c oxidase assembly protein 17 10672474-10698375 Disease related genes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA021565, HPA021579 Supportive Supportive Nucleus Expressed in all colon: 17.4 SCO2 MYP6, SCO1L ENSG00000130489 SCO2 cytochrome c oxidase assembly protein 22 50523568-50526439 Disease related genes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA056254 Uncertain Supportive Nucleus but not nucleoli, Mitochondria Expressed in all bone marrow: 27.3 SCP2 ENSG00000116171 Sterol carrier protein 2 1 52927229-53051703 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA027101, HPA027135, HPA027317 Supportive Supportive Vesicles, Nucleus but not nucleoli, Cytoplasm Expressed in all liver: 442.1 SDHA FP, SDH2, SDHF ENSG00000073578 Succinate dehydrogenase complex, subunit A, flavoprotein (Fp) 5 218241-256700 Citric acid cycle related proteins, Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB034929, HPA041981, HPA064582 Supportive Supportive Mitochondria Expressed in all heart muscle: 217.1 SDHAF2 C11orf79, FLJ20487, PGL2, SDH5 ENSG00000167985 Succinate dehydrogenase complex assembly factor 2 11 61430042-61447529 Cancer-related genes, Disease related genes, Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA039464, HPA039732 Supportive Expressed in all lymph node: 26.9 SDHB SDH, SDH1 ENSG00000117118 Succinate dehydrogenase complex, subunit B, iron sulfur (Ip) 1 17018722-17054170 Cancer-related genes, Citric acid cycle related proteins, Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA002868, CAB009822, CAB068233, CAB068234, CAB068235 Supportive Supportive Mitochondria, Nucleus but not nucleoli, Plasma membrane Expressed in all heart muscle: 136.8 SDHC PGL3 ENSG00000143252 Succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa 1 161314257-161375340 Cancer-related genes, Citric acid cycle related proteins, Disease related genes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Expressed in all kidney: 96.0 SDHD PGL, PGL1 ENSG00000204370 Succinate dehydrogenase complex, subunit D, integral membrane protein 11 112086773-112120013 Cancer-related genes, Citric acid cycle related proteins, Disease related genes, FDA approved drug targets, Mitochondrial proteins, Predicted membrane proteins, Predicted secreted proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA045727 Uncertain Expressed in all kidney: 142.7 SFXN1 FLJ12876 ENSG00000164466 Sideroflexin 1 5 175477062-175529742 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA019543, HPA063745 Uncertain Supportive Mitochondria Expressed in all liver: 45.7 SFXN2 ENSG00000156398 Sideroflexin 2 10 102714538-102743492 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA018150, HPA026834 Supportive Uncertain Mitochondria Tissue enhanced 0 kidney: 11.3 placenta: 3.0 SFXN3 SFX3 ENSG00000107819 Sideroflexin 3 10 101031234-101041244 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA008028, HPA048105 Uncertain Supportive Mitochondria Expressed in all small intestine: 27.9 SFXN4 ENSG00000183605 Sideroflexin 4 10 119140767-119165667 Disease related genes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA018028, HPA020872 Supportive Supportive Vesicles Expressed in all thyroid gland: 25.3 SFXN5 BBG-TCC ENSG00000144040 Sideroflexin 5 2 72942036-73075619 Mitochondrial proteins, Predicted membrane proteins, Predicted secreted proteins Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA015473, HPA056866 Uncertain Uncertain Nucleus but not nucleoli, Mitochondria Mixed cerebral cortex: 18.0 SH3BP5 Sab ENSG00000131370 SH3-domain binding protein 5 (BTK-associated) 3 15254853-15341368 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA036445 Uncertain Expressed in all adrenal gland: 130.7 SH3GLB1 Bif-1, CGI-61, KIAA0491, PPP1R70 ENSG00000097033 SH3-domain GRB2-like endophilin B1 1 86704570-86748184 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB004650, HPA015608, HPA019900 Supportive Supportive Cytoplasm Expressed in all testis: 92.7 SHC1 p66, SHC ENSG00000160691 SHC (Src homology 2 domain containing) transforming protein 1 1 154962298-154974395 Mitochondrial proteins, Predicted intracellular proteins, RAS pathway related proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA001844, CAB005374, CAB016305 Supportive Supportive Cytoplasm, Nucleoli Expressed in all gallbladder: 82.3 SHMT2 SHMT ENSG00000182199 Serine hydroxymethyltransferase 2 (mitochondrial) 12 57229327-57234935 Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA020543, HPA020549 Supportive Supportive Mitochondria, Cytoskeleton (Microtubules) Expressed in all liver: 59.8 SIRT3 SIR2L3 ENSG00000142082 Sirtuin 3 11 215458-236931 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA026809, CAB037142 Uncertain Expressed in all testis: 15.1 SLC25A1 CTP, SLC20A3 ENSG00000100075 Solute carrier family 25 (mitochondrial carrier; citrate transporter), member 1 22 19175575-19178830 Disease related genes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA030183 Uncertain Expressed in all duodenum: 71.0 SLC25A10 DIC ENSG00000183048 Solute carrier family 25 (mitochondrial carrier; dicarboxylate transporter), member 10 17 81712236-81721016 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA023048 Supportive Expressed in all kidney: 42.8 SLC25A11 OGC, SLC20A4 ENSG00000108528 Solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11 17 4937130-4940251 Mitochondrial proteins, Plasma proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA021167 Uncertain Expressed in all heart muscle: 128.2 SLC25A12 Aralar ENSG00000115840 Solute carrier family 25 (aspartate/glutamate carrier), member 12 2 171784370-171999859 Disease related genes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA035333, HPA035334 Supportive Uncertain Nucleus but not nucleoli, Cytoplasm Expressed in all skeletal muscle: 46.4 SLC25A13 ARALAR2, CITRIN, CTLN2 ENSG00000004864 Solute carrier family 25 (aspartate/glutamate carrier), member 13 7 96120220-96322147 Disease related genes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA018997 Uncertain Supportive Mitochondria Expressed in all liver: 46.5 SLC25A14 BMCP1, UCP5 ENSG00000102078 Solute carrier family 25 (mitochondrial carrier, brain), member 14 X 130339888-130373361 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins, Predicted secreted proteins, Transporters Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA060316 Uncertain Mitochondria Expressed in all cerebral cortex: 10.0 SLC25A15 D13S327, HHH, ORC1, ORNT1 ENSG00000102743 Solute carrier family 25 (mitochondrial carrier; ornithine transporter) member 15 13 40789412-40810111 Disease related genes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA042146 Uncertain Expressed in all duodenum: 31.5 SLC25A16 D10S105E, GDA, HGT.1, ML7 ENSG00000122912 Solute carrier family 25 (mitochondrial carrier), member 16 10 68477999-68527474 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA044580 Uncertain Expressed in all adipose tissue: 7.5 SLC25A18 ENSG00000182902 Solute carrier family 25 (glutamate carrier), member 18 22 17563439-17590994 Mitochondrial proteins, Plasma proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level Group enriched 8 adipose tissue: 9.0;cerebral cortex: 35.3;liver: 18.1 testis: 2.7 SLC25A19 DNC, MCPHA, MUP1, TPC ENSG00000125454 Solute carrier family 25 (mitochondrial thiamine pyrophosphate carrier), member 19 17 75272981-75289510 Disease related genes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Expressed in all testis: 27.9 SLC25A2 ORNT2 ENSG00000120329 Solute carrier family 25 (mitochondrial carrier; ornithine transporter) member 2 5 141302629-141304045 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level HPA042146 Uncertain Tissue enriched 57 testis: 5.7 adipose tissue: 0.0 SLC25A20 CAC, CACT ENSG00000178537 Solute carrier family 25 (carnitine/acylcarnitine translocase), member 20 3 48856931-48898993 Disease related genes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA016862, HPA029863 Uncertain Supportive Cytoplasm, Mitochondria Expressed in all duodenum: 45.8 SLC25A21 ODC, ODC1 ENSG00000183032 Solute carrier family 25 (mitochondrial oxoadipate carrier), member 21 14 36677921-37172866 Mitochondrial proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA000662 Uncertain Tissue enhanced 0 bone marrow: 4.3;testis: 4.5 thyroid gland: 1.3 SLC25A22 EIEE3, FLJ13044, GC1, NET44 ENSG00000177542 Solute carrier family 25 (mitochondrial carrier: glutamate), member 22 11 790475-798316 Disease related genes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA014662 Uncertain Supportive Mitochondria, Nucleus but not nucleoli Tissue enhanced 0 cerebral cortex: 39.2 pancreas: 10.5 SLC25A23 APC2, FLJ30339, MGC2615 ENSG00000125648 Solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 23 19 6436079-6465203 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA050883 Uncertain Expressed in all cerebral cortex: 64.8 SLC25A24 APC1, DKFZp586G0123 ENSG00000085491 Solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 24 1 108134036-108200849 Mitochondrial proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA028519, HPA063636 Uncertain Supportive Mitochondria Expressed in all rectum: 28.8 SLC25A25 KIAA1896, MCSC, PCSCL ENSG00000148339 Solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 25 9 128068201-128109245 Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA020381 Uncertain Supportive Mitochondria, Vesicles Expressed in all gallbladder: 37.3 SLC25A26 ENSG00000144741 Solute carrier family 25 (S-adenosylmethionine carrier), member 26 3 66133610-66388116 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA026887 Supportive Supportive Mitochondria Expressed in all thyroid gland: 26.3 SLC25A27 FLJ33552, UCP4 ENSG00000153291 Solute carrier family 25, member 27 6 46652915-46678193 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level CAB009508 Uncertain Mixed ovary: 32.8 SLC25A28 MRS3/4, MRS4L ENSG00000155287 Solute carrier family 25 (mitochondrial iron transporter), member 28 10 99610522-99620609 Mitochondrial proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level Expressed in all testis: 46.8 SLC25A29 C14orf69, FLJ38975 ENSG00000197119 Solute carrier family 25 (mitochondrial carnitine/acylcarnitine carrier), member 29 14 100291111-100306547 Mitochondrial proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA030781 Uncertain Expressed in all thyroid gland: 87.0 SLC25A3 PHC ENSG00000075415 Solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3 12 98593591-98606379 Disease related genes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA045709 Supportive Mitochondria, Nucleus, Nucleoli Expressed in all heart muscle: 427.8 SLC25A30 ENSG00000174032 Solute carrier family 25, member 30 13 45393316-45418455 Mitochondrial proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA045260 Uncertain Uncertain Nucleus but not nucleoli Expressed in all heart muscle: 37.7 SLC25A31 ANT4, DKFZP434N1235 ENSG00000151475 Solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 31 4 127730378-127774299 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA015064, HPA016841 Uncertain Supportive Mitochondria Tissue enriched 441 testis: 44.1 adipose tissue: 0.0 SLC25A32 MFTC ENSG00000164933 Solute carrier family 25 (mitochondrial folate carrier), member 32 8 103398635-103415189 Mitochondrial proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA047402 Uncertain Expressed in all lymph node: 16.2 SLC25A33 BMSC-MCP, MGC4399, PNC1 ENSG00000171612 Solute carrier family 25 (pyrimidine nucleotide carrier), member 33 1 9539482-9585179 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA049982 Uncertain Mixed testis: 4.9 SLC25A34 DKFZp781A10161 ENSG00000162461 Solute carrier family 25, member 34 1 15736405-15741396 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at transcript level HPA069806 Supportive Mitochondria Tissue enhanced 0 duodenum: 10.9;small intestine: 10.5 skeletal muscle: 6.1 SLC25A35 FLJ40217 ENSG00000125434 Solute carrier family 25, member 35 17 8287763-8295343 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA051720 Uncertain Uncertain Mitochondria, Vesicles Mixed testis: 12.0 SLC25A36 FLJ10618, PNC2 ENSG00000114120 Solute carrier family 25 (pyrimidine nucleotide carrier ), member 36 3 140941830-140979933 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA027036 Uncertain Uncertain Cytoplasm, Mitochondria, Nucleus Expressed in all endometrium: 37.1 SLC25A37 MFRN, MFRN1, MSCP ENSG00000147454 Solute carrier family 25 (mitochondrial iron transporter), member 37 8 23528805-23575463 Mitochondrial proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA045680 Uncertain Expressed in all bone marrow: 71.8 SLC25A38 FLJ20551 ENSG00000144659 Solute carrier family 25, member 38 3 39383348-39397351 Disease related genes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA041027 Uncertain Expressed in all thyroid gland: 28.1 SLC25A39 CGI-69, FLJ22407 ENSG00000013306 Solute carrier family 25, member 39 17 44319625-44324870 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at transcript level Evidence at transcript level Evidence at transcript level HPA026785 Uncertain Expressed in all bone marrow: 160.8 SLC25A4 ANT1, PEO2, PEO3, T1 ENSG00000151729 Solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4 4 185143241-185150382 Disease related genes, FDA approved drug targets, Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA060665 Uncertain Group enriched 5 heart muscle: 161.8;skeletal muscle: 60.1 cerebral cortex: 21.3 SLC25A40 MCFP ENSG00000075303 Solute carrier family 25, member 40 7 87833568-87876357 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA055197 Uncertain Expressed in all lymph node: 9.1 SLC25A41 APC4, FLJ40442, MGC34725 ENSG00000181240 Solute carrier family 25, member 41 19 6426037-6433779 Mitochondrial proteins, Predicted intracellular proteins, Transporters Evidence at transcript level Evidence at transcript level Evidence at transcript level HPA043591 Uncertain Tissue enhanced 0 testis: 1.5 cerebral cortex: 0.5 SLC25A42 MGC26694 ENSG00000181035 Solute carrier family 25, member 42 19 19063999-19112888 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA049449 Uncertain Supportive Mitochondria Expressed in all kidney: 28.9 SLC25A43 ENSG00000077713 Solute carrier family 25, member 43 X 119399060-119454478 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at transcript level Evidence at transcript level Evidence at transcript level HPA035188 Uncertain Uncertain Nucleus Mixed esophagus: 16.1 SLC25A44 FLJ90431, KIAA0446 ENSG00000160785 Solute carrier family 25, member 44 1 156193932-156212796 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level Expressed in all cerebral cortex: 22.2 SLC25A45 ENSG00000162241 Solute carrier family 25, member 45 11 65375192-65383701 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at transcript level HPA050821 Uncertain Uncertain Nucleus but not nucleoli, Cytoplasm Expressed in all lymph node: 9.1 SLC25A46 ENSG00000164209 Solute carrier family 25, member 46 5 110738136-110765161 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA047605, HPA067558 Supportive Nucleus, Mitochondria Expressed in all tonsil: 19.1 SLC25A47 C14orf68 ENSG00000140107 Solute carrier family 25, member 47 14 100323337-100330378 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at transcript level Evidence at transcript level Evidence at transcript level Tissue enriched 238 liver: 99.8 duodenum: 0.4 SLC25A5 2F1, ANT2, T2, T3 ENSG00000005022 Solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 5 X 119468400-119471319 FDA approved drug targets, Mitochondrial proteins, Plasma proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA060665 Uncertain Expressed in all duodenum: 586.9 SLC25A51 CG7943, MCART1, MGC14836 ENSG00000122696 Solute carrier family 25, member 51 9 37879400-37904353 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA058261, HPA058273 Uncertain Expressed in all adipose tissue: 7.8 SLC25A52 MCART2 ENSG00000141437 Solute carrier family 25, member 52 18 31759562-31760880 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at transcript level Evidence at transcript level Evidence at transcript level HPA058261, HPA058273 Uncertain Tissue enriched 40 testis: 7.8 adipose tissue: 0.1 SLC25A53 MCART6 ENSG00000269743 Solute carrier family 25, member 53 X 104099214-104157027 Mitochondrial proteins, Predicted membrane proteins Evidence at transcript level Evidence at transcript level Evidence at transcript level HPA034959 Uncertain Mixed lymph node: 1.4 SLC25A6 ANT3, ANT3Y, MGC17525 ENSG00000169100 Solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 6 X 1386152-1392724 FDA approved drug targets, Mitochondrial proteins, Plasma proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA060665 Uncertain Expressed in all salivary gland: 216.7 SLC27A3 ACSVL3, FATP3, MGC4365 ENSG00000143554 Solute carrier family 27 (fatty acid transporter), member 3 1 153774354-153780157 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at transcript level Evidence at protein level HPA006935, HPA067508 Uncertain Uncertain Endoplasmic reticulum Expressed in all lung: 21.7 SLC9A6 KIAA0267, NHE6 ENSG00000198689 Solute carrier family 9, subfamily A (NHE6, cation proton antiporter 6), member 6 X 135985439-136047264 Disease related genes, Mitochondrial proteins, Potential drug targets, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA059445, HPA059590 Uncertain Supportive Vesicles Expressed in all cerebral cortex: 37.8 SLC9B2 FLJ23984, NHA2, NHEDC2 ENSG00000164038 Solute carrier family 9, subfamily B (NHA2, cation proton antiporter 2), member 2 4 103019868-103085829 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA047008 Uncertain Uncertain Nucleus but not nucleoli, Cell Junctions Mixed cerebral cortex: 15.3 SLIRP C14orf156, DC50 ENSG00000119705 SRA stem-loop interacting RNA binding protein 14 77708071-77761104 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA020291 Uncertain Supportive Mitochondria Expressed in all heart muscle: 124.6 SMCP MCSP ENSG00000163206 Sperm mitochondria-associated cysteine-rich protein 1 152878317-152885047 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at transcript level HPA035105 Supportive Tissue enriched 526 testis: 361.0 cerebral cortex: 0.6 SMDT1 C22orf32, DDDD, dJ186O1.1 ENSG00000183172 Single-pass membrane protein with aspartate-rich tail 1 22 42079691-42084284 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA032117, HPA060340 Uncertain Supportive Mitochondria, Nucleus Expressed in all ovary: 20.3 SOD2 ENSG00000112096 Superoxide dismutase 2, mitochondrial 6 159669057-159762529 Cancer-related genes, Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA001814, CAB002013 Supportive Expressed in all bone marrow: 567.3 SPATA19 CT132, FLJ25851, SPAS1, spergen1 ENSG00000166118 Spermatogenesis associated 19 11 133840631-133845538 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA040082 Supportive Tissue enriched 368 testis: 60.2 tonsil: 0.1 SPATA5 AFG2, SPAF ENSG00000145375 Spermatogenesis associated 5 4 122923074-123319450 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA036450, HPA036451 Supportive Mixed testis: 2.1 SPG7 CAR, CMAR, SPG5C ENSG00000197912 Spastic paraplegia 7 (pure and complicated autosomal recessive) 16 89490917-89557768 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Expressed in all thyroid gland: 28.6 SPNS1 HSpin1, LAT, nrs, PP2030, SPIN1, SPINL ENSG00000169682 Spinster homolog 1 (Drosophila) 16 28974221-28984548 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041995, HPA042988 Supportive Uncertain Golgi apparatus, Vesicles, Nucleoli, Cytoplasm Expressed in all placenta: 17.9 SQRDL CGI-44 ENSG00000137767 Sulfide quinone reductase-like (yeast) 15 45631148-45691294 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA017079, HPA041589 Supportive Supportive Mitochondria Expressed in all colon: 143.8 SSBP1 mtSSB, SSBP ENSG00000106028 Single-stranded DNA binding protein 1, mitochondrial 7 141738321-141787922 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA002866 Supportive Supportive Mitochondria Expressed in all tonsil: 127.0 STAR StAR, STARD1 ENSG00000147465 Steroidogenic acute regulatory protein 8 38143649-38151265 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA023644, HPA027318, CAB032598 Supportive Tissue enriched 13 adrenal gland: 1770.2 ovary: 139.9 STARD13 ARHGAP37, DLC2, GT650, LINC00464 ENSG00000133121 StAR-related lipid transfer (START) domain containing 13 13 33103135-33350630 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA039535, HPA058867 Supportive Uncertain Nucleoli, Nuclear membrane, Cytoplasm Mixed placenta: 18.2 SUCLA2 ENSG00000136143 Succinate-CoA ligase, ADP-forming, beta subunit 13 47936487-48001326 Citric acid cycle related proteins, Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA039435, HPA039536, HPA061528 Supportive Supportive Mitochondria Expressed in all skeletal muscle: 59.2 SUCLG1 ENSG00000163541 Succinate-CoA ligase, alpha subunit 2 84423523-84460045 Citric acid cycle related proteins, Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA036683, HPA036684 Supportive Supportive Mitochondria, Plasma membrane Expressed in all kidney: 265.9 SUCLG2 ENSG00000172340 Succinate-CoA ligase, GDP-forming, beta subunit 3 67360460-67654614 Citric acid cycle related proteins, Enzymes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA046705, HPA051998 Supportive Supportive Plasma membrane, Mitochondria, Nucleus, Microtubule organizing center Expressed in all colon: 107.8 SUOX ENSG00000139531 Sulfite oxidase 12 55997180-56006641 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA038208, HPA038209 Uncertain Expressed in all kidney: 31.0 SUPV3L1 SUV3 ENSG00000156502 Suppressor of var1, 3-like 1 (S. cerevisiae) 10 69180232-69209099 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA038380, HPA038405 Supportive Expressed in all testis: 14.7 SURF1 ENSG00000148290 Surfeit 1 9 133351755-133356676 Disease related genes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA021029, CAB033946 Uncertain Expressed in all fallopian tube: 43.2 SYNJ2BP Arip2 ENSG00000213463 Synaptojanin 2 binding protein 14 70366496-70417061 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA000866 Uncertain Supportive Uncertain Mitochondria Expressed in all kidney: 15.6 TAMM41 C3orf31, DKFZp434E0519, MGC16471 ENSG00000144559 TAM41, mitochondrial translocator assembly and maintenance protein, homolog (S. cerevisiae) 3 11790442-11846919 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA036834, HPA044861 Uncertain Uncertain Cytoplasm Expressed in all ovary: 9.2 TARS2 FLJ12528, TARSL1 ENSG00000143374 Threonyl-tRNA synthetase 2, mitochondrial (putative) 1 150487364-150507609 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA028626 Uncertain Uncertain Nucleus but not nucleoli, Cytoplasm, Cytoskeleton (Intermediate filaments) Expressed in all tonsil: 13.0 TFAM TCF6, TCF6L2 ENSG00000108064 Transcription factor A, mitochondrial 10 58385022-58399221 Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins, Transcription factors Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA040648, HPA063684 Supportive Supportive Mitochondria Expressed in all testis: 36.9 TFB1M CGI-75, mtTFB ENSG00000029639 Transcription factor B1, mitochondrial 6 155257509-155314493 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA029428 Uncertain Expressed in all adrenal gland: 12.2 TFB2M FLJ22661, FLJ23182, Hkp1 ENSG00000162851 Transcription factor B2, mitochondrial 1 246540560-246566324 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA028482, HPA030265, HPA061095 Uncertain Supportive Mitochondria Expressed in all adrenal gland: 18.7 TIMM10 TIM10, TIM10A ENSG00000134809 Translocase of inner mitochondrial membrane 10 homolog (yeast) 11 57528463-57530803 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA039946 Supportive Supportive Mitochondria Expressed in all tonsil: 39.4 TIMM10B FXC1, TIM10B, Tim9b ENSG00000132286 Translocase of inner mitochondrial membrane 10 homolog B (yeast) 11 6481447-6484679 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA052265 Uncertain Expressed in all thyroid gland: 26.2 TIMM13 Tim13, TIMM13B ENSG00000099800 Translocase of inner mitochondrial membrane 13 homolog (yeast) 19 2425624-2427894 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA048985 Uncertain Supportive Mitochondria, Nucleoli Expressed in all duodenum: 35.6 TIMM17A TIM17, TIM17A ENSG00000134375 Translocase of inner mitochondrial membrane 17 homolog A (yeast) 1 201955491-201970661 Cancer-related genes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA010083 Uncertain Supportive Nucleus but not nucleoli, Mitochondria Expressed in all adrenal gland: 40.6 TIMM17B DXS9822, JM3 ENSG00000126768 Translocase of inner mitochondrial membrane 17 homolog B (yeast) X 48893447-48898143 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA029093 Uncertain Uncertain Cytoskeleton (Microtubules), Mitochondria Expressed in all heart muscle: 30.9 TIMM21 C18orf55, HSPC154, TIM21 ENSG00000075336 Translocase of inner mitochondrial membrane 21 homolog (yeast) 18 74148511-74160530 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA010587, HPA051543 Uncertain Uncertain Nucleus but not nucleoli Expressed in all heart muscle: 20.1 TIMM22 TEX4 ENSG00000177370 Translocase of inner mitochondrial membrane 22 homolog (yeast) 17 997117-1003671 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA045138 Uncertain Expressed in all placenta: 8.0 TIMM23 TIM23 ENSG00000265354 Translocase of inner mitochondrial membrane 23 homolog (yeast) 10 45972449-46003734 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level HPA031408 Uncertain Supportive Mitochondria Expressed in all testis: 70.5 TIMM23B bA592B15.7 ENSG00000204152 Translocase of inner mitochondrial membrane 23 homolog B (yeast) 10 49942033-49974850 Mitochondrial proteins, Predicted membrane proteins Evidence at transcript level Evidence at transcript level No evidence Expressed in all bone marrow: 7.5 TIMM44 TIM44 ENSG00000104980 Translocase of inner mitochondrial membrane 44 homolog (yeast) 19 7926718-7943920 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA043052 Supportive Supportive Mitochondria Expressed in all heart muscle: 16.4 TIMM50 TIM50L ENSG00000105197 Translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae) 19 39480412-39493785 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA048843, HPA056448 Supportive Supportive Nucleus but not nucleoli, Mitochondria Expressed in all testis: 48.5 TIMM8A DDP, DFN1, MTS ENSG00000126953 Translocase of inner mitochondrial membrane 8 homolog A (yeast) X 101345661-101349196 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA003628 Supportive Supportive Mitochondria Mixed liver: 4.4 TIMM8B DDP2, FLJ21744, MGC102866, MGC117373, TIM8B ENSG00000150779 Translocase of inner mitochondrial membrane 8 homolog B (yeast) 11 112084800-112086798 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041173 Supportive Expressed in all heart muscle: 25.5 TIMM9 TIM9A ENSG00000100575 Translocase of inner mitochondrial membrane 9 homolog (yeast) 14 58408494-58427614 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA002932 Uncertain Supportive Mitochondria Expressed in all esophagus: 26.3 TK2 ENSG00000166548 Thymidine kinase 2, mitochondrial 16 66508003-66552544 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041162 Uncertain Expressed in all adipose tissue: 31.4 TMEM126A DKFZp586C1924, OPA7 ENSG00000171202 Transmembrane protein 126A 11 85647967-85656547 Disease related genes, Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA046648 Uncertain Uncertain Cytoplasm, Nucleus Expressed in all heart muscle: 40.2 TMEM143 FLJ10922 ENSG00000161558 Transmembrane protein 143 19 48332356-48364237 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA014476 Uncertain Uncertain Nucleoli Expressed in all skeletal muscle: 24.1 TMEM8B C9orf127, NAG-5, NGX6 ENSG00000137103 Transmembrane protein 8B 9 35814451-35854847 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at protein level HPA052130, HPA062701 Uncertain Uncertain Vesicles Expressed in all ovary: 14.5 TMLHE BBOX2, FLJ10727, TMLH, XAP130 ENSG00000185973 Trimethyllysine hydroxylase, epsilon X 155490115-155669944 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA034589, HPA040331 Uncertain Supportive Mitochondria Expressed in all heart muscle: 14.1 TOMM20 KIAA0016, MAS20, MOM19, TOM20 ENSG00000173726 Translocase of outer mitochondrial membrane 20 homolog (yeast) 1 235109336-235128936 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB005585, HPA011562 Supportive Supportive Mitochondria Expressed in all thyroid gland: 118.2 TOMM20L UNQ9438 ENSG00000196860 Translocase of outer mitochondrial membrane 20 homolog (yeast)-like 14 58395916-58408701 Mitochondrial proteins, Predicted membrane proteins Evidence at transcript level Evidence at transcript level Evidence at transcript level HPA044997 Uncertain Tissue enriched 23 testis: 5.2 colon: 0.2 TOMM22 TOM22 ENSG00000100216 Translocase of outer mitochondrial membrane 22 homolog (yeast) 22 38681948-38685421 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA003037 Supportive Supportive Mitochondria Expressed in all tonsil: 23.4 TOMM34 HTOM34P, TOM34 ENSG00000025772 Translocase of outer mitochondrial membrane 34 20 44942130-44960486 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA018845, HPA056875 Supportive Supportive Cytoplasm Expressed in all testis: 98.4 TOMM40 C19orf1, D19S1177E, PER-EC1, PEREC1, TOM40 ENSG00000130204 Translocase of outer mitochondrial membrane 40 homolog (yeast) 19 44890569-44903689 Mitochondrial proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB009156, HPA036231, HPA036232 Supportive Supportive Mitochondria, Cytoplasm Expressed in all esophagus: 14.3 TOMM40L FLJ12770, TOMM40B ENSG00000158882 Translocase of outer mitochondrial membrane 40 homolog (yeast)-like 1 161225939-161230744 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level HPA051304 Uncertain Expressed in all heart muscle: 12.7 TOMM7 ENSG00000196683 Translocase of outer mitochondrial membrane 7 homolog (yeast) 7 22812628-22822852 Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins, Predicted secreted proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level Expressed in all ovary: 560.5 TOMM70A KIAA0719 ENSG00000154174 Translocase of outer mitochondrial membrane 70 homolog A (S. cerevisiae) 3 100363431-100401398 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA014589, CAB017156, HPA048020 Supportive Supportive Mitochondria Expressed in all cerebral cortex: 27.1 TOP1MT ENSG00000184428 Topoisomerase (DNA) I, mitochondrial 8 143304384-143359979 Enzymes, FDA approved drug targets, Mitochondrial proteins, Predicted intracellular proteins, Predicted secreted proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA001915, HPA021542 Uncertain Supportive Mitochondria Expressed in all ovary: 25.3 TRAP1 HSP75, HSP90L ENSG00000126602 TNF receptor-associated protein 1 16 3651639-3717597 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041082, HPA044227 Supportive Supportive Mitochondria Expressed in all fallopian tube: 62.4 TRIT1 FLJ20061, IPT ENSG00000043514 TRNA isopentenyltransferase 1 1 39841022-39883511 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA024174, HPA053686 Uncertain Uncertain Nucleus, Cytoplasm, Golgi apparatus Expressed in all fallopian tube: 13.6 TRMT10C FLJ20432, MRPP1, RG9MTD1 ENSG00000174173 TRNA methyltransferase 10 homolog C (S. cerevisiae) 3 101561862-101566446 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA036671 Uncertain Supportive Mitochondria, Nucleus but not nucleoli Expressed in all lymph node: 18.2 TRMU FLJ10140, MTO2, TRMT ENSG00000100416 TRNA 5-methylaminomethyl-2-thiouridylate methyltransferase 22 46330875-46357340 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA035273, HPA043300 Uncertain Supportive Mitochondria, Nucleus but not nucleoli Expressed in all adrenal gland: 5.6 TRNT1 CCA1, CGI-47, MtCCA ENSG00000072756 TRNA nucleotidyl transferase, CCA-adding, 1 3 3126916-3150879 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA036938 Uncertain Supportive Mitochondria Expressed in all prostate: 13.6 TSFM EF-TS, EF-Tsmt ENSG00000123297 Ts translation elongation factor, mitochondrial 12 57782589-57808071 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA006204 Supportive Supportive Mitochondria, Nucleus Expressed in all adrenal gland: 37.9 TSPO BZRP, DBI, IBP, MBR, mDRC, PBR, pk18, PKBS ENSG00000100300 Translocator protein (18kDa) 22 43151514-43163242 Cancer-related genes, FDA approved drug targets, Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB011232, HPA046260 Uncertain Supportive Mitochondria, Nuclear membrane, Cytoplasm, Vesicles Expressed in all bone marrow: 241.0 TST RDS ENSG00000128311 Thiosulfate sulfurtransferase (rhodanese) 22 37010859-37020183 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA003044, HPA003643, CAB009546 Supportive Supportive Mitochondria Expressed in all colon: 110.7 TUFM EF-TuMT, EFTu ENSG00000178952 Tu translation elongation factor, mitochondrial 16 28842411-28846408 Disease related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA018991, HPA024087, CAB075730, CAB075731 Supportive Supportive Mitochondria Expressed in all kidney: 84.1 TXN2 MT-TRX ENSG00000100348 Thioredoxin 2 22 36467036-36482030 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA000994, CAB008681 Supportive Supportive Mitochondria Expressed in all adrenal gland: 82.6 UCP1 SLC25A7, UCP ENSG00000109424 Uncoupling protein 1 (mitochondrial, proton carrier) 4 140559434-140568805 Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level CAB037199 Uncertain Tissue enriched 12 adrenal gland: 2.5 heart muscle: 0.2 UCP2 BMIQ4, SLC25A8 ENSG00000175567 Uncoupling protein 2 (mitochondrial, proton carrier) 11 73974667-73983307 Mitochondrial proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at transcript level Evidence at protein level CAB025583 Uncertain Expressed in all lymph node: 305.9 UCP3 SLC25A9 ENSG00000175564 Uncoupling protein 3 (mitochondrial, proton carrier) 11 74000281-74009435 Disease related genes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level CAB010771 Uncertain Nucleus but not nucleoli, Plasma membrane, Cytoplasm Tissue enriched 23 skeletal muscle: 49.8 esophagus: 2.1 UNG DGU, HIGM4, UDG, UNG1, UNG2 ENSG00000076248 Uracil-DNA glycosylase 12 109097574-109110992 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB011605 Uncertain Uncertain Cytoplasm Expressed in all adrenal gland: 37.6 UQCR11 QCR10, UQCR ENSG00000127540 Ubiquinol-cytochrome c reductase, complex III subunit XI 19 1597172-1605490 Mitochondrial proteins, Predicted membrane proteins Evidence at protein level Evidence at transcript level Evidence at transcript level Evidence at protein level Expressed in all skeletal muscle: 73.5 UQCRB QCR7, QP-C, UQBP, UQCR6 ENSG00000156467 Ubiquinol-cytochrome c reductase binding protein 8 96225920-96235634 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA043060 Uncertain Expressed in all heart muscle: 446.5 UQCRC1 D3S3191, QCR1, UQCR1 ENSG00000010256 Ubiquinol-cytochrome c reductase core protein I 3 48599002-48610976 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA002815, HPA003525, CAB033782 Supportive Supportive Mitochondria, Cytoplasm Expressed in all skeletal muscle: 76.1 UQCRC2 QCR2, UQCR2 ENSG00000140740 Ubiquinol-cytochrome c reductase core protein II 16 21952660-21983660 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA007998, HPA019146 Supportive Supportive Mitochondria Expressed in all heart muscle: 239.1 UQCRFS1 RIP1, RIS1, RISP, UQCR5 ENSG00000169021 Ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1 19 29205321-29213541 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA041863, HPA050339 Supportive Supportive Mitochondria Expressed in all skeletal muscle: 47.0 UQCRH QCR6, UQCR8 ENSG00000173660 Ubiquinol-cytochrome c reductase hinge protein 1 46303631-46316776 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA042574 Supportive Expressed in all heart muscle: 122.1 UQCRQ QCR8, QP-C, UQCR7 ENSG00000164405 Ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa 5 132866560-132868031 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA046693, HPA053323 Uncertain Supportive Mitochondria Expressed in all heart muscle: 318.4 VAMP1 SYB1, VAMP-1 ENSG00000139190 Vesicle-associated membrane protein 1 (synaptobrevin 1) 12 6462237-6470987 FDA approved drug targets, Mitochondrial proteins, Predicted membrane proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB002779, CAB016119 Uncertain Expressed in all bone marrow: 34.5 VARS2 DKFZP434L1435, G7a, KIAA1885, VARS2L, VARSL ENSG00000137411 Valyl-tRNA synthetase 2, mitochondrial 6 30908242-30926459 Disease related genes, Enzymes, Mitochondrial proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA062449, HPA070267 Uncertain Uncertain Mitochondria Expressed in all cerebral cortex: 13.1 VDAC1 MGC111064, PORIN ENSG00000213585 Voltage-dependent anion channel 1 5 133971915-134005133 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level CAB005885, HPA030780 Supportive Uncertain Cytoplasm Expressed in all skeletal muscle: 187.6 VDAC2 ENSG00000165637 Voltage-dependent anion channel 2 10 75210154-75231448 Mitochondrial proteins, Predicted intracellular proteins, Transporters Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA043475 Supportive Supportive Mitochondria Expressed in all heart muscle: 43.5 VDAC3 HD-VDAC3 ENSG00000078668 Voltage-dependent anion channel 3 8 42391624-42405897 Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA026864 Uncertain Supportive Mitochondria Expressed in all skeletal muscle: 200.1 WARS2 TrpRS ENSG00000116874 Tryptophanyl tRNA synthetase 2, mitochondrial 1 119031216-119140671 Enzymes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA069692 Supportive Mitochondria, Nucleus but not nucleoli, Plasma membrane Expressed in all fallopian tube: 9.8 WWOX FOR, SDR41C1, WOX1 ENSG00000186153 WW domain containing oxidoreductase 16 78099413-79212667 Disease related genes, Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA050992 Uncertain Supportive Golgi apparatus, Cytoplasm Expressed in all thyroid gland: 59.1 XAF1 BIRC4BP, HSXIAPAF1, XIAPAF1 ENSG00000132530 XIAP associated factor 1 17 6755447-6775647 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA057302 Uncertain Uncertain Nucleus, Mitochondria Mixed spleen: 53.2 YARS2 CGI-04, FLJ13995, mt-TyrRS ENSG00000139131 Tyrosyl-tRNA synthetase 2, mitochondrial 12 32727490-32755902 Disease related genes, Enzymes, Mitochondrial proteins, Plasma proteins, Potential drug targets, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA038721, HPA057610 Uncertain Expressed in all tonsil: 6.7 YME1L1 ENSG00000136758 YME1-like 1 ATPase 10 27110112-27155266 Enzymes, Mitochondrial proteins, Predicted intracellular proteins, Predicted membrane proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA066953 Uncertain Supportive Mitochondria, Nucleus but not nucleoli Expressed in all thyroid gland: 62.8 YRDC FLJ23476, IRIP, SUA5 ENSG00000196449 YrdC N(6)-threonylcarbamoyltransferase domain containing 1 37802944-37808185 Mitochondrial proteins, Predicted intracellular proteins Evidence at protein level Evidence at transcript level Evidence at protein level Evidence at protein level HPA030147 Uncertain Uncertain Mitochondria Expressed in all bone marrow: 24.4 YWHAE FLJ45465 ENSG00000108953 Tyrosine 3-monooxygenase/tryptophan 5-monooxygenase activation protein, epsilon 17 1344272-1400378 Cancer-related genes, Mitochondrial proteins, Plasma proteins, Predicted intracellular proteins Evidence at protein level Evidence at protein level Evidence at protein level Evidence at protein level HPA008445, CAB016200, CAB021109, CAB047350 Supportive Uncertain Cytoplasm Expressed in all cerebral cortex: 357.2